Ola kinoLapaau

Congenital vascular pathology. aortarctia

Aortic coarctation mea he hou o kona wahi. A like ano pili i ka congenital abnormalities.

E like me ko oukou ike ana, ma ka aortic koko hele i na ipu a pau o ka naau. I ka wā o ka hou hapa haawi pilikia.

E like me ka hana pono E hoike mai, coarctation o ka aorta mea loa, he pono ole i loko o kanaka me kekahi kāna hana o ka aaiaoe ano (e like Turner maʻi pale). Kēia kina paha kekahi e kekahi hapa o ka congenital anomaly artery kiwikā.

It E e hoʻomaopopo i ka coarctation o ka aorta ua manaoia e ia i ka loa, he pono ole congenital kāna hana o ka mea'ōnaehana mānowai koko'ōnaehana, detectable mai ka hānauʻana a hiki i ka makahiki o he kanaha.

Kēia kina hiki no hoi i hoʻomaka ai ma ka hui pu ana, a me nā anomalies. Ka loa, he pono ole poʻe loaʻa:

  • pathology o mitral aortic kiwikā ;
  • me hoʻokahi wale naau ventricle;
  • 'āno'ē interventricular septum.

I ka hoike ana o symptoms hilinaʻi nui ma luna o ka hana, e hele ana oukou ma ka hou hapa o ka ipu koko ka leo i loko o ka kekahi wā. Ke alo aku o nā malformations o ka mea'ōnaehana mānowai koko'ōnaehana aggravate wale keʻano.

E like me ka loina hōʻike symptoms i nā lā mua o ke ola i loko o ka hola hapalua o na kamalii uuku ka poe i diagnosed me coarctation o ka aorta.

Mehana a pau i wehewehe aku ma ka wa e kaawale aku o ka maʻi symptoms a adolescence.

Na hoailona o ka maʻi i:

  • maʻule hou ihola nō;
  • pōniuniu;
  • nosebleed;
  • headaches;
  • anu wawae paha mau wawae;
  • pokole o ka hanu;
  • cramps ma na wawae a me ka hoomahuahua i ke koko, iloko o physical exertion;
  • umauma eha;
  • pōkole kiekie;
  • retardation o? acaeoey;
  • luhi ma hope hoʻokō '.

Eia naʻe, e makaala i ka lapaʻau hoike ana mai o ka maʻi i hoi ma kahi ee.

Coarctation o ka aorta. lapaʻau

Ma ka hapanui o na hihia o ka ka loaʻaʻana o ka maʻi i loko o keiki paipaiʻoki kino ma hope o ka pōkole wā a koke. Mua o nā mea a pau, o ka moku'āina i'ōleloʻia ai stabilizing ai '.

I ka diagnosing maʻi ma mua na makahiki a me ka hana ua hoike mai. Eia naʻe, ma ka hoomaopopo ana i ka nui mehana symptoms, hoʻomanawanui iki mai i ka manawa e hoomakaukau ai no ka 'uao.

Maʻoki kino, ua wehe i ka hou aorta. No ka nui like 'ole uuku o kona kina ua weheʻia, i nā wēlau o ka moku ua pili. Kēia hana o kaʻoki lāʻau lapaʻau lapaʻau ua kapaia anastomosis. Inā pono, ka wehe 'ana i ka nui mahele o ka nui hoʻohana dacron pakuiia auanei lakou a me kekahi hapa o ka artery o ke ahonui, e compensate no na anomalies.

Ma pohihihi keia hoopii, hoʻonui angioplasty i ke hoʻohana. Akā, i kēia hana ua wehewehe aku ma ka pae kiʻekiʻe o ka hoʻolako 'ole.

Mua na keiki i koi 'ia ai' i ka pāʻana ke koko. Ma na hihia, e like me ka Inc ua hoakaka ia no ke ola.

Ka maʻi hiki ke eliminated me ke kōkua o keʻoki kino. E like me ka hana pono E hoike mai, ma ka hapanui o na hihia, nalo na symptoms ma hope o hana koke lawa.

Ma keia hihia, kiʻekiʻe pilikia o ka make ma luna o ke kāʻei kua o ka mea'ōnaehana mānowai koko pilikia, me, a ma hope oʻoki kino. Inā untreated, ka hapanui o na nā mea maʻi e make ai ma mua o ka makahiki o ke kanaha. Kokoke mau, ka hana ua hana ma kaʻuʻuku mai.

It E e hoʻomaopopo i ka hou ke'ākoʻakoʻa ma muli o ka emi ana o elasticity o ka'aʻaʻa i loko o ka ipu pa. Ma keia hihia, he aneurysm hiki ke hana. hiki i nā elue no kona muli malama like sclerosis o ka aorta. Iapaau ana o keia maʻi i kekahi, ua hōʻikeʻoki lāʻau lapaʻau.

Coarctation o ka aorta hiki ole ke Hāʻule maila lākou. Poe akamai i paipai aku ua hoʻonānā mau a, e ka pono e ala mai, e i kanaka me ke kali ole.

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