Erythremia - He aha ka keia? ke kahua eritremii

Erythremia - he 'ano o ke koko kāna hana wehewehe aku ma ka hoʻonuiʻana (overgrowth) o erythrocytes, a ia mea ulu ma ka helu o nā aeee (leucocytes, platelets). Anei i ka maʻi, pinepine benign maʻi mea he pohihihi keia. He aka e hiki degeneration o benign malignant leukemia. Erythremia - he maʻi i mea maʻi e pili ana 4 kanaka mai o 100 miliona kanaka o ka makahiki. Ia, aole ia e hilinai i hoohanau, akā, ka mea, ua ana diagnosed i kanaka mua a me ka mua. Oiai olelo hihia o ka maʻi ma ka makahiki kaikaina, pinepine na wahine.

Erythremia (pā'ālua ICD10 - S94.1) i ka maʻi papa.

Koko keena, aʻano papa hana o ka maʻi

eritremiiʻano papa hana e hoʻomōhala ana i like penei.

Red koko keena - ula koko keena, nona ka papa kuhikuhi hana - o ka amo ana o o oxygen i na keena a pau o ko mākou kino. Ka mea, i hua mai la i loko o ka iwi lolo, spleen a me ka akepaʻa. Iwi ka lolo mea i loko o ka iwi lōʻihi, vertebrae, o kona iwiʻaoʻao, sternum a me ka iwi poʻo iwi. 96% o kaʻulaʻula koko keena i piha me ka hemoglobin, i hāpai mai i ka ÷ naehana hanu kuleana pili i. Red kala like 'ole e hāʻawi mai ai ia hao. Red koko aeee i hanaʻia ma ka hoʻohana 'ana i anei i keena. Lākou kiʻiona hiki - ka hiki e puunaue (paʻi), lilo iho i loko o kekahi 'ē halepaahao.

Nā iwi i ka yellow a me ka iwi ka lolo, i ua poe e momoma'aʻaʻa. He hoʻomaka e paka koko hehee wale nō i loko o loa keia, ka wā 'ē aʻe kumu o ka hematopoietic i hana i ko lakou mau oihana.

Erythremia (ICD-10 - International Mea Maluna o ka Maʻi, ma a ka eiae ia a hiki i keia maʻi 94,1 C) - he maʻi pathogenesis ua ole i maopopo. No ka kumu nō,ʻaʻole möakäka hou maopopo ma poe kumu, i ke kino hoʻomaka e vigorously paka ulaula koko aeee i mea ole hou pono i loko o ke koko, mahuahua koko (viscosity), a hoʻomaka e lilo ke koko clots. Over manawa, e māhuahua hypoxia (oxygen pololi). Ke keena mai i loaa e pono no kou kino, he malfunction ia lŘlŘ i loko o ka nohona ma'ōnaehana o ke kino.

A mau hana hoihoi kūʻiʻo e pili ana i eritremii

1. Erythremia - keia mea he benign maʻi no a pau leukemias. Ia mea he lōʻihi manawa ia mea OE a wale ma hope hiki aku ai i ka complications.
2. Ua hiki e asymptomatic, a aole i hai aku ia ia iho no na makahiki.
3. I loko nō o ka mahuahua nui o ka platelets, e hoomanawanui i prone i excessive kahe ana ke koko.
4. Erythremia i ka 'ohana mōʻaukala, no laila, inā he' ohana i ka maʻi, i ka pilikia o ka helehelena o ka pili mahuahua.

kumu eritremii

Like nā 'ano o ka leukemia, nō i maopopo hoomaopopo erythremia, a me na kumu no kona hanana ka mea, i ka weheia. Eia naʻe, Kupanaha kumumea i mea conducive i kona muli:

1. Aaiaoe predisposition.
2. ʻawahia waiwai trapped i loko o ke kino.
3. Ionizing pāhawewe.

aaiaoe predisposition

Ua ua i ike pono i'ōewe mutations i ka helehelena eritremii, nae, ka mea i loaʻa i loko o ka 'ohana maʻi ia lŘlŘ pinepine lawa i ka kela mau hanauna. Ke likelihood o ulu i ka maʻi ua mahuahua ma kekahi mau manawa, ina he kanaka ka hoomanawanui.

• Down maʻi pale ( 'aʻe' ana o ka maka, a me ka'ā'ī, developmental lohi);
• Klinefelter ka maʻi pale (hiki disproportionate huahelu, a developmental 'ole' ana);
• Ua pua i nā maʻi pale (haʻahaʻa kiʻekiʻe, pigmentation ma luna o ka maka, a me kona disproportionate? Acaeoey predisposition i oncological maʻi);
• Marfan maʻi pale (kāna hana o connective'aʻaʻa).

Predisposition e eritremii wehewehe ia e ka mea i ka aaiaoe ke kelepona hele hana (me ke koko pa alima) i lolelua ka, no laila, he kanaka i susceptible i mawaho hopena maikaʻi 'ole o ka - toxins, pāhawewe.

pāhawewe

ʻO ka X-Ray a me ka gamma-kukuna i hapa 'ia' ke kemu ma ke kino, me ka hoohuoi ana i ka aaiaoe keena. Ka mea, e make paha mutate.

Naʻe, i ka loa mana radioactive pāhawewe loaa e ka poʻe i hana 'aʻai chemotherapy o ka maʻi, e like me ka pono me ka poe ma ka epicenter o ka mana kanu a me'ātoma hopeʻia.

ʻawahia waiwai

I ko kino, ka mea, e hiki hoi o na la aaiaoe mutation o aeee. Mau konohiki i kapaia Nine Inch mutagens. Ma hope o haʻawina lehulehu, kńnaka Ua loaʻa i nā mea maʻi eritremii hoʻokaʻaʻike me kēia mau waiwai ma mua o ke kūpono 'ana o ka maʻi. Mau waiwai nā:

• benzene (loaʻa i loko o ka haku mele 'ana o ke kakolina a me ka nui Nine Inch nā'uheheʻe);
• antibacterial konohiki (i loko o nui, "Chloramphenicol");
• cytostatic konohiki (Anati-ʻeho).

Eritremii kahua o ka hoʻonaʻauao a me kā lākou mau symptoms

Erythremia i ka kēia mau kapuwai: loiloi mua, wehewehe nui loa aku a me ka maʻi. Kēlā me kēia no ia i kona mau symptoms. Ka loiloi mua ke kahua me ke ī hope no ka makahiki me ka hoike ana i kekahi symptoms nui. Nā hana symptoms o nā mea maʻi i hookuu hewa ia ma luna o ka mea 'ē aʻe, emi hoʻoponopono illnesses. Ma hope o nā mea a pau, i kauka pinepine mai i uku lawa ka noonoo imperfect koko hoao i.

Inā he mea he iniiaiie erythremia, koko e ho'āʻo ai i lōpū deviations mai ke kūmau.

Ka loiloi mua ke kahua me ka i wehewehe aku ma ka luhi, pōniuniu, tinnitus. Ke hoomanawanui hiamoe poorly, Kahalaopuna anu i loko o kaʻaoʻao, ma laila e haanou ana mai o na lima a me na wawae. A emi i ka noʻonoʻo hana. No mawaho hoike ana mai o ka maʻi nae. Headache uaʻaʻole noʻonoʻo i kekahi hoailona o ka maʻi, aka, ia ia lŘlŘ i ka loiloi mua kahua no ka ilihune holo i loko o ka lolo. No keia kumu, hoemiia hihio, maliu a me ka akamai. A hiki i kaʻike, o "erythremia" symptoms o ka maʻi i loko o ka lua o ke kahua i kā lākou mauʻano - kahe ana ke koko nui aʻe ana, lilo ae la ia he uuku hematoma. Ma ka lalo wāwae i ikea pouli mau kiko (thrombosis symptoms) a i na mai hehe. Ulu nā loko e paka ulaula koko keena - ka spleen a me ka akepaʻa. Aie i ke kūpono 'ana o ka maʻi pehu lymph aka wahi.

Eritremii lua o ke kahua i hope ma kahi o 10 makahiki. Ke kaumaha ua me ka nui loa hoemiia. Ka ili loaʻa kamako iki leo (IeAUPIIe, IAa IO mau lima a me na wawae), ka pahee kīleo hoʻololi waihoʻoluʻu a pau, paa - mālama i kona kahiko waihoʻoluʻu. Maneo bothered ka hoʻomanawanui i ua listen ma hope o auau ana i ka mehana a me ka wai wela. Ke kino i ka pehu aa koko mai ka overabundance o ke koko, o ka oi aku i loko o ka'ā'ī. Mau maka ua bloodshot, no ka mea, erythremia, i mea nui i loko o ka lua o ke kahua i nā symptoms o ka a, ka paipai 'ana i ke koko kahe i na ipu o ka maka.

Ma muli o ka ilihune koko holo i loko o ka capillaries hoike eha a me ka aa ana ka waiʻona ma loko o na manamana a me nā manamana wāwae. I holomua na lilo ia i mea maopopo tsiatonicheskie pūkoʻa ia ma luna o lākou.

Aia mau iwi a me ka epigastric eha. Oleloʻeha pili me gouty ano o ka oi uricʻakika. I mau, i ka hana o ka puʻupaʻa ua Nyos, pinepine diagnosed pyelonephritis, a loaʻa uratovye hakuʻala pohaku.

ʻO ko mākou hopohopo nenoaiu poino. Ke ahonui ko mākou hopohopo, o kona naʻau i loko mea lolelua, wehewehe aku ma ka tearfulness a me ka loli pinepine.

(viscosity) o ka mea, piʻi pū koko, i nā hualoaʻa ma ke ano o ke koko clots i loko o nā vascular wahi. No hoi he mea i ka pilikia o ka ulu varicose aa koko ulu.

Aʻo! Hoʻomanawanui iki mai i kekahi hana eha iaʻi mai ka hypertension, a me ka wehe ana o ulcers i loko o ka duodenum. O ke kumu ho i ka emi ma ke kino i ka pale aku ia lakou, a hoomahuahua i ka helu o Helicobacter pylori - o keia bacterium ke kumu ulcers.

Eritremii ke kolu o ke kahua Ua wehewehe aku ma pallor o kaʻili, pinepine maule ana, nawaliwali a me ka sluggishness. Malama hooloihi ae i kahe ana ke koko ma ka palena haʻahaʻa poino, anaemia aplastic no i haʻahaʻa hemoglobin pae i loko o ke koko.

Ke kolu o ke kahua eritremii: Symptoms a me Complications

Erythremia - koko maʻi, a ma ke kolu o ke kahua iʻano pākīkē. Ma keia ke kahua, ka iwi lolo keena undergo fibrosis. He hiki ole paka ulaula koko keena, no laila, na rula o ke koko keena haule, i kekahi manawa, i ka noho pilikia nā hoailona. Ma ka lolo, eia foci o ka hoopalupaluia, akepaʻa fibrosis huli no. Ka laau awaawa, bladder mea he manoanoa, h ÷ bile a me ka pigment na pohaku. ʻO ka hopena o ka cirrhosis a me vascular occlusion.

Mua, ka mea, i mahuahua thrombus ke lilo i kumu o ka make ana o nā mea maʻi me ka erythema. malalo iho e hoʻololi moku paia, aia no he blockage o aa koko i loko o ka lolo, spleen, ka naʻau a me nā wāwae. Aicieeaao occlusive mai - blockage o na moku o nā wāwae a me ka pilikia o ka piha contraction.

Hakuʻala ka pōʻino. Aie i ka ulu ana o uricʻakika nā mea maʻi e ae mai ke ami hoi eha gouty külana.

Aʻo! I ka eritremii wāwae a me nā lima pinepine hoʻololi waihoʻoluʻu. Ke hoomanawanui Ua prone e bronchitis a me ke anu.

i ka maʻi

Erythremia - he kali hoʻi koʻu maʻi. Ka maʻi hele mai i loko o kona mau lohi, ka mea, o ka hoʻomaka o ka holumua ai a me ka unobtrusive ano. Nā mea maʻi pinepine ola no ka makahiki me ka uku noonoo ana i ka nīnūnē symptoms. Eia naʻe, ma ka oi kaumaha hihia no ka mea, o ka ke koko clots make ke'ākoʻakoʻa i loko o 4-5 makahiki.

A me ka eritremii mahuahua spleen. Kaʻawale palapala me ka cirrhosis lesion a me ka diencephalon. Ma allergic maʻi, a me ka infectious complications i e ho ohana ana, nā mea maʻi pinepine hiki ole tolerate kekahi ai 'pae i ae mai urticaria a me nāʻili maʻi. Papa o ka maʻi ua huikau ma ke kākoʻo '-i hana keia,ʻike, ua ana i hope o ka kūpuna.

Posteritremichesky myelofibrosis - he rebirth o ka benign papa o ka maʻi i loko o malignant. Ke ano o ke kumu i loko o nā mea maʻi i ola a hiki i kēia wā. Ma kēia hihia, na kauka ae aku i erythremia loaaʻeho külana.

He loa nui e pono diagnose erythremia a kūpono lapaʻau. ʻike, ka loaʻa o ka helu o nā haʻawina.

Ka Ikepili o ke koko ma eritremii

A hiki i kaʻike, o "erythremia" koko ho'āʻo kiko'î i mea nui no kaʻike,, ua hanaia ma ka wahi mua. Mua a poʻokela keia mea he like koko hōʻike. He'āno'ē i loko ona e lilo i mua poʻe hiamoe bele. Ua hoʻomāhuahuaʻoe i ka helu o ka ula koko keena. Initially, ia mea i noho pilikia, nae, a me ka hooulu ana i ka maʻi no ka hana nui a me ka nui, a kau mai maluna o ka hope ke kahua. Ka mea maʻamau erythrocyte pae i loko o ke koko o ka wahine mea mai ka 3.5 hiki i 4.7, a me na kanaka - mai ka 4 a hiki i 5.

Inā diagnosed erythremia, koko ho'āʻo na kii i ka hōʻike 'ka hoomahuahua i ka ula koko keena, wahi e pili ana i ka AYEIE mahuahua ma ka hemoglobin. Hematocrit hoike ana i ke koko o ka hana, e lawe oxygen, mahuahua ia 60-80%. Kala like 'ole' inideka ua ole hoʻololi, akā, i ke kolu o ke kahua hiki e aku i kekahi mea - maʻamau, mahuahua paha hoemiia. Platelets a keʻokeʻo koko keena mahuahua. White koko keena ulu kekahi mau manawa, a me kekahi manawa hou aku. Hoʻomanaʻo eosinophils (kekahi manawa me basophils) maoli. Seriously mahuahua platelets. Erythrocyte sedimentation kōmi - i oi aku mamua o 2 mm o / hora.

Auwe, piha koko helu, ina pono no ka loiloi muaʻike, wahi ike, a me ka wale ma luna o ka muli o kānaʻike, ua i waiho.

Other haʻawina ma eritremii

• Biochemical Ka Ikepili o ke koko. Kona pahuhopu nui - e hooholo i ka nui o ka hao i loko o ke koko, a me ka nui o ke akepaʻa kuleana pili i ho'āʻo ma - AST a me ka Alt. Ka mea, i hookuu, mai ke akepaʻa, i loko o ka make ana o kona keena. Hoʻoholo 'ana o ka nui o ka bilirubin Hōʻike ka oolea o ke kaʻina hana o ka erythrocyte luku.
• Iwi ka lolo puncture. Ka Ikepili ia me ke kuikele i ua hookomoia i loko o kaʻili i ka periosteum. Na Huaolelo Hōʻike i ke kūlana o ka hematopoietic aeee i loko o ka iwi lolo. Research Hōʻike i ka helu ana o aeee i loko o ka lolo, i ke alo o ka maʻi 'aʻai keena, a fibrosis (ulu o connective'aʻaʻa).
• I ka wā i hana i kaʻike, o ka "maʻi erythremia" keʻena hoʻokolohua hōʻailona, a me nā abdominal ultrasound. Ultrasound hōʻike congested nā loko, hoonee aku i ake a me ka spleen, e like meʻekeʻeke o fibrosis i loko o ia mau mea.
• Doppler Hōʻike koko māmā holo, a kōkua i kuhikuhi i ke koko clots.

eritremii lapaʻau

It E e kaulana ia erythremia pinepine progresses lohi, a mai ka benign papa. Mua o nā mea a pau, i aʻo aku ai iā kauka e e Aloha Hawaii loli - hou ia e ke ao o waho, e hele, e kiʻi maikaʻi Emotions (endorfinoterapiya kekahi manawa ea i nui nā hualoaʻa). Products i pihaʻi me kekahi hapa o ka nui nui o ka hao, a me ka wikamina C, E e hoʻokoe '.

Ma ke kahua mua o ka maʻi i ka papa kuhikuhiE manao o kaʻike, "erythremia" - ke koko kiko'î a emi i ka maʻamau hemoglobin - mai i 150-160, a me ka hematocrit - ia 45-46. Ua mea i nui, e hōʻole i nā complications, kena ae la ia e ka maʻi - kāna hana o ke koko holo,ʻeha ma nā manamana lima, a pela aku ...

Normalize hematocrit me ka hemoglobin kōkua kahe ana ke koko, a ma keia hihia ua hoʻohana 'ia i kēia lā. Naʻe, i kēia ke kaʻina hana no ua hana i loko o ka? Aieao o ka pilikia, no ka mea, stimulates ka iwi lolo a me ka thrombopoiesis hana (platelet ho okumu kaʻina). Aia Ua i kekahi kaʻina hana i kapaia eritrotsitaferez, i mea e huikala ai i ke koko o ka ula koko keena. Ma keia hihia, i ke koko wai koko koe.

ka lapaʻauʻia

Cytostatics - keia ano antitumor ai 'a i hoʻohana ma complications eritremii - ulcers, thrombosis, cerebral holo kāna hana i kupu mai i loko o ka lua o ke kahua o ka maʻi. "Mielosan", "busulfan", hydroxyurea, "Imifos" radioactive phosphorus. Ka hope ua noʻonoʻo mana ma ka mea i loaa i loko o ka iwi, a inhibits lolo kuleana pili i.

Steroid i hoakaka ia no ka hemolytic anaemia o autoimmune kumu. "Prednisolone" Ua oi loa aku hoi mahalo. Inā ka iapaau ana, aole ia e haawi hualoaʻa e pili, i hoakaka iaʻoki kino, e wehe i ka spleen.

E pale hao deficiency, hao pakuʻi ai i ke koi 'ia - "gemofer", "Totem", "Sorbifer".

ʻO kēia pūʻulu o ka ai 'i hoakaka ia e like me ka ai:

1. Antihistamines.
2. Hakumakuma ke koko.
3. Anticoagulant (koko thinning).
4. Hepatoprotectors.

Erythremia, ua pinepine lawe lapaau mai i loko o ka haukapila - mea he maʻi nui ka mea e hookomo i ka hailona o complications. He nui ka hōʻike i kakahiaka nui me hiki, a hoʻomaka kona nohoʻana.