Pancytopenia - he pathological ano ma i emi ma ke koko ai hoʻolahaʻia o nā kumu o ka haku mele 'ana. Kumu, symptoms, lapaʻau

Kekahi hooulu ana o ka maʻi i loko o ke kino, ke kumu o ka loli ma ka hana, mai kaʻike ākea koko. Eia naʻe, loaʻa nō ka nui o nā pathologies no i ka loli i ka papa kuhikuhiE lapaʻau hiʻona. Pancytopenia - o kekahi o ka pathological keʻano o ka hanaʻana o ka hematopoietic'ōnaehana, a ua hoakakaia ma ka kuokoa maʻi, a hiki ia i ka hōʻike o nā concomitant nosological.

General manaÿo

Ka maʻi mea ole, he pono ole, no laila, eʻike nōʻo ia ia i ka kŰia loa kanaka. Pancytopenia - He moku'āina o deficiency o ke koko keena, i ka ulu ana o ka a ua kauoha aku e abnormalities i loko o ka 'ole o ka precursor koko keena ma ke kahua o ka hematopoiesis. Hoemiia pae o kaʻulaʻula koko keena, keʻokeʻo koko keena, a platelets aie i ka mea i ke kumu aeee hiki ponoʻole,ʻaʻole kuleana pili i.

I ka maʻi e hoʻomōhala ana i loko o nā 'ano apau loa:

• idiopathic, kena ae la ma na aʻe;
• kiʻekiʻe, a ua kauoha aku e mawaho ololi.

A pathological ano ma kahi o 50% o ka hihia e hoʻomōhala ana i autoimmune type. Ia mea, i ke kino ua kaua wale me kou koko keena, kuhi ia no na konohiki. Idiopathic palapala ke ala mai e ku e ia IeIIeYOA o ka hou mawaho ololi e hōʻeleu i ke adverse hoʻokūkū.

Pancytopenia - he maʻi e hiki ke ili, ulu i kekahi manawa i ka wa a ke keiki i loko o ka opu. A keiki ua hanau mua me kāna hana o ke koko-ho okumu i nā loko. Ua hiki e congenital a me ka iwi lolo hypoplasia, no laila, i ka'ōnaehana hiki ole Makuakane me kā lākou mau hana.

Ke etiology o ka maʻi a me ka kamepiula kumumea

Mawaena o ka papa kuhikuhiE kumu o ka hooulu ana o ka maʻi e aaiaoe mutations, lōʻihi-makahiki hoʻohana 'ana ai', radioactive aʻawahia loa. Idiopathic palapala ua wehewehe aku ma ka mea i hiki ole i ke kumu e hookupaa, akā naʻe, he mau hihia o ka maʻi ma hope o ka hanau keiki ana.

E kukulu ana i na kumu ia mea nui no ka maikaʻi hoʻokūkū. Ke kāpaeʻana i ka mawaho io keiki i loko o kēia maʻi - 50% pomaikai kōmi.

Ma waho aʻeo i ke kumu nui ka mea, he mau aʻe e hoʻonui ai i ke kūpono 'ana o ke pathology:

• E hana me ka benzene paha arsenic;
• Fanconi anemia;
• ka mea hoʻomaʻi ano o ka maʻiʻaʻai;
• chemotherapy;
• antibiotics a me immunosuppressants;
• autoimmune maʻi e like me systemic lupus erythematosus;
• radiotherapy.

Fanconi anaemia - kekahi o ka etiological aʻe o ka pancytopenia. E hoʻomōhala ana i ma luna o ke kāʻei kua o congenital anomalies ua noʻonoʻo pono i autosomal recessive maʻi. Anemia ua wehewehe aku ma ke alo o ka mā ma ka apana o nā polokina kuleana no ka DNA? Aiiio a me ka chromosome friability.

Ka lapaʻau kiʻi o ka maʻi

Pathological ano hoike mai ai ia ia iho i loko o ka palapala o ka ekolu syndromes. Kēlā me kēia no kēia mau ano hiʻona e emi i ka helu ana o kekahi 'ano o ke koko keena. Leukopenia ua hoike mai i ke kiʻi o ka huʻi sepsis a me ka muli o ulcer-necrotic keʻano o ka hanaʻana o kaʻili, a mucous membranes.

Erythropenia a me na hiohiona ka ho'ēmiʻana i loko o hemoglobin hoʻonāukiuki aku i ke kūpono 'ana o nā symptoms o ka anemia. Kēia moku'āina Ua wehewehe aku e:

• mae o ka ili integument;
• lele mua o kona maka ;
• pōniuniu;
• tinnitus;
• nawaliwali, a me ka luhi;
• nawaliwali ka hoomaopopo ana.

E hoomanawanui i ohumu o ka pokole o ka hanu a me ka naau palpitations. Auscultation e hooholo voiceless naʻau nanahe, systolic'ōhumu mai ma luna o ka holoʻokoʻa ili o ka naau wānana, i ka leo o ka luna o ka jugular aa koko. Worsening o ka hoʻomanawanui kaʻano kumu loli ma ka electrocardiogram, a hōʻike i ke kūpono 'ana o ka naʻau ole.

Thrombocytopenia ua hoikeia aku ai e pinepine kahe ana ke koko (epistaxis, gastrointestinal, uterine), kahe ana ke koko nui aʻe ana, i keʻano o ka petechiae a me hemorrhages i loko o kaʻili. Huʻi symptoms o ka maʻi i mālama no e pili ana i ka mahina, a pinepine alakai i ka make. Maʻi pancytopenia 'ae' oi maikaʻi, a mai ka emi hai symptoms

i ka maʻi ua manaoia e lilo no ka loa eiiieaena. Pancytopenia, a complications i oi, he pono ole no ka poʻeʻelemākule, pu ma keʻano o nā mea palahēhē a me kahe ana ke koko.

PalekanaEND_LINK ana

Ka hihia mua pono kōkua i ka hoʻomalu nana, ohi mōʻaukala a me ke ola o ka hoʻomanawanui. Hou kohoia CBC. Ma ka hihia o kēia nā hoailona ke noonoo i ka hooulu ana o ka pancytopenia, a hoʻomaka hou PalekanaEND_LINK ana:

• leukocytes <2 m 109 / ho'āo ai;
• platelets <150 m 109 / L;
• erythrocytes <3,5 m 109 / ho'āo ai.

Ia like puncture iwi ka lolo, i Ho'ākāka 'i ke alo o'āno'ē keena a me myelokaryocytes. Nānā 'ia ma ke alo o abnormalities, a me ka iwi lolo hypoplasia. No hoi e paa ana ia hemolytic Eia kekahi laʻana.

pancytopenia lapaʻau

Pākōlea mauʻanuʻu hilinaʻi ma ka lapaʻau hihia, i ke ahonui o ka ana a me ka etiological ololi e kena ae i ka maʻi. ʻO kēia lapaʻau ano hiki ke hoʻohana:

• Koko transfusion, e koe i ka koena o ka palapala kumu.
• Transplantation o ka iwi ka lolo a me anei i keena. Pinepine hana i loko o nā mea maʻi opiopio a me ka waena makahiki.
• Ma ka hihia o autoimmune pancytopenia lawelawe immunosuppressant palapala noi "Cytoxan", "Methylprednisolone," "Neoral", "Sandimun".
• O ia hoʻi, noho haumāna kahi o ka iwi lolo, e hana - "Neupogen", "Neulasta", "Procrit", "Leukin".

lāʻau kanu

Ka luna 'maʻi Inc ka loaʻa o ka hoʻohana' ana o ka lāʻau lapaʻau lapaau. hiki ke hoala mai i ka nui o kaʻulaʻula koko keena, a hemoglobin me ke kōkua o nā hua. Paʻa i kī i i ke kanaka ma muli o ka lehu,ʻeleʻele currants, ala puhaka, strawberries, hua, apricot. Ka hao waiwai turnips, gooseberries, cherries a me nā hua waina, me ka ai ana o ka i makemake ole ke koena wale i ke koena o ke koko keena, akā, i hooikaika mai i ka'ōnaehana paleʻea nenoaiu.

A helu o ke kanaka epekema no ka hana maikaʻi pancytopenia maupaʻa ka meli. Ua Ua hui me ka kēia huahana.

• me ka waina a me ka Aloe;
• kālika;
• ota;
• lemona, maloo apricots, paʻi hua waina, e paʻipaʻi i a me walnuts.

Paʻa mea nui loa i ka infusions a me decoctions o ka lāʻau lapaʻau lau nahele paʻapū paʻapū, birch, mauu kumu wahine, clover, dandelion, orchids, clover, buckwheat.

ka hopena

Pancytopenia - he mea maʻi, a equates i ka make maʻi. Maikaʻi hoʻokūkū hilinaʻi nui ma luna o ka oolea o ka lapaʻau na hoailona, ano a me nā kahua o ka hoʻonaʻauao o? Acaeoey ma i lapaau hoʻomaka. Oia maʻi ka hiki pono o ka pale ma mua o ka daimonio.

I ka makahiki 'inikua ninaninau ana o ka heluna kanaka ka poʻea pau i ka' ike o ka pathological ana i loko o ke kakahiaka kahua o ka hoʻonaʻauao. Ma kekahi pili keia i keʻena hoʻokolohua ninaninau ki ina hana like.