Ola kinoMaʻi a me nā kūlana

Polycythemia - polycythemia mea ...: Symptoms a me ka lapaʻau

Polycythemia - he maʻi maʻi i loko i ka maʻiʻo, piʻi pū ula koko aeee (ula koko aeee) i loko o ke koko. No hoi, ka wā e like me ka pathology i loko o 70% o nā mea maʻi loli aʻe i ka helu ana o platelets a me leukocytes i loko o ka nui ala.

Ka maʻi Aʻole ole i ke kiʻekiʻe prevalence - makahiki no miliona heluna aaeno i hou aku elima wā. Loa pinepine i ka maʻi e hoʻomōhala ana i polycythemia waena-elemakule a me ka poʻeʻelemākule kanaka. Wahi a ka 'ikepili helu, he poe kane e ae aku i kēia kāna hana i elima mau manawa hou ma mua o nā wāhine pinepine. I kēia lā, he kokoke nana i keia wahi me polycythemia, symptoms a me ka hana o ka maʻi i hoakakaia ma lalo nei.

Nā kumu o ka maʻi

Polycythemia - he pili-malignant maʻi. I ka lā, i ka mau kumu o ka maʻi mea IKE OLE IA. Ka mea, ua manao ia o ka maʻi oia hoi, kena ae la ia e mutations aʻoʻia kuikawa iwi lolo'ūhū. Aaiaoe loli alakai i excessive mahele a me ka ulu ana o ke koko keena, pakahi aku la ia ula koko keena.

Mea Maluna o ka maʻi

Mau pūʻulu o ka maʻi.

  • Polycythemia vera a Vakeza maʻi, i ua ma ka huli māheleʻia i loko o ka puke Paipala i (a laila, hana me he kuokoa maʻi) a me ka haumāna (haumāna polycythemia e hoʻomōhala ana i aie i ka maʻi akemāmā maʻi, hikoko, hydronephrosis, ma ua leha kiekie).

  • Pili polycythemia (stress ole wahahee) - ina keia moku'āina o ka nui o kaʻulaʻula koko keena ma ka maʻamau laulā.

Polycythemia: symptoms o ka maʻi

Loa pinepine, i ka maʻi i asymptomatic. I kekahi manawa, e like me ka hopena o ke anamanaʻo no ka mea okoa kumu ia paha e accidentally hoikeia polycythemia. Symptoms, a e hoʻolohe, e nana i e hiki mai ana.

? Anoe? O subcutaneous aa koko

I ka polycythemia ma luna o kaʻili, loa pinepine i loko o ka'ā'ī, dilated subcutaneous aa koko hōʻike ma. Me keia maʻi o ka ili i ulaula kamako iki waihoʻoluʻu a pau, o ka oi aku kekahi 'ma ka hamama mau o ke kino -'ā'ī, i na mea kaua, i lalo ke alo. Ke mucousʻili lahilahi o na lehelehe a me ka elelo mea bluish-ula kala like 'ole,' oiaʻiʻo ma loko o ka maka ua bloodshot.

Ua ke kumu no hoʻololi i loko o ke koko hoʻohālana, waiwai ula koko keena, a pau na moku ili a me ka meheu o kona rheological waiwai (māmā holo), no laila, i ka bulk o ka hemoglobin (ula pigment) ia iho i loko o ka hoemi palapala ( 'o ia hoʻi, malalo iho o Nine Inch loli) a me ka hoʻololi waihoʻoluʻu.

maneo

Kokoke hapalua o na nā mea maʻi e loaa ana mai ka polycythemia, aia no he ikaika ka ohane, pakahi aku la ia mea ma hope o ka lawe ana i ka mehana bata. O kŰia lawelawe 'ana me kekahi mau' ano o ke polycythemia vera. Maneo ia lŘlŘ manawa, e kuu ana i hana 'ona i loko o ke koko, i ka nui histamine, i mea hiki ke hoʻonui i ka ili capillaries, e alakai i ka mahuahua koko i loko o ia mau mea, a me ka nānā aku ana i ho'ākāka' ia ka waiʻona ma ke.

Eritromelalagiya

O kŰia ua wehewehe aku ma ka ikaika loa pōkole-makahiki eha i loko o ka fingertips. Hoʻonāukiukiʻana mai o lākou mea ulu ma platelets i loko o nā ipu uuku o na lima, kūpono ma ka ho okumu o ka lehulehu microthrombuses, plugging arterioles a ālai 'i ke kahe o ke koko a hiki i na nā'aʻaʻa o ka manamanalima. Mawaho nā hiʻona e like me ke ano hoi redness a me ka nānā aku ma luna o kaʻili o bluish mau kiko. No ka mea, o ka mea o hikiʻole i thrombosis paipai aspirin.

Splenomegaly (hoʻonui o ka spleen)

Ma waho o ka spleen, ake, a me ka hiki ke hoʻololi, a he oiaio, ua nui kona. Mau kino i pili 'ole i loko o ke kahua a me ka luku ana o ke koko keena. Mahuahua i ka lehulehu o ka hope hiki aku ai i ka hua i loko o ke ake, a spleen.

Duodenal ulcers a me ka'ōpū

Ua olaʻoki lāʻau lapaʻau pathology e hoʻomōhala ana i aie i ka poe liilii, moku thrombosis digestive'āpana mucousʻili lahilahi. Ka hopena o ka huʻi circulatory kāna hana ka necrosis (necrosis) kino paia kuleana, a ho okumu ma kona kahua o ka ulcer. Eia hou kekahi, hoemiia ia'ku i gastric helicobacter (he microorganism hoomokuahana ulcer a me ka gastritis).

Ke koko clots ma nui o na moku

He nui prone i keia mai o ka lalo lala aa koko. Thrombi, ka uhaʻiʻana aku , mai ka moku pa hiki, piliwaiwai i ka naau, e komo i loko o ka pulmonary holo (maʻiʻaʻai) a i pulmonary embolism (pulmonary embolism) - he ano incompatible me ke ola.

kahe ana ke koko nui aʻe ana

I loko nō o ka mea i ka helu ana o platelets iʻike ākea koko loli a maoli he kona coagulation, me ka polycythemia kānāwai gingival kahe ana ke koko.

gout

Ma pae kiʻekiʻe o uricʻakika paʻakai ona, i waihoia ma kekahi mau ami, a hoʻonāukiuki i kaʻoi eha.

  • Pain i loko o na lala. Kēia symptom ke kumu no poho wāwae arteries, hou ia, a, me ia i kaʻilihune, hune holo. Kēia pathology ua kapaia "occlusive maʻi"
  • Pain i loko o ka iwi palahalaha. Mahuahua iwi lolo hope (? Acaeoey makahiki o ke koko aeee) stimulates ka pā lonoaʻili o lalo iwi i me mechanical stress.

Ka mea hōʻemi o ka mau ana o ka meaola

Ma ia he maʻi like polycythemia, symptoms paha e like me symptoms o'ē aʻe kāna hana (e like, anaemia): headaches, ikaika luhi, tinnitus, vertigo, huali, "tingling" i mua o nā maka, pokole o ka hanu, flushing ana o ke koko a hiki i ke poo. Hoomahuahua ae la lakou i ke koko (viscosity) waiwai haʻalele no uku 'naoh ipu, e like me ka hopena, he mea he mahuahua i loko o ke koko,. A pau keia maʻi pinepine i complications e like me ka naʻau o ka hoʻokō 'ole a me ka mikrokardioskleroza (hakahaka o connective'aʻaʻa o ka naau Muscle, hoopiha ana i na kina, akā,' aʻole e hana i ka mea i hana ').

lapaʻau '

Polycythemia hoike aku i ka hopena o kekahi mau koko Ka Ikepili, i loaʻa:

  • nui helu oʻulaʻula keena mai 6,5 e 7,5 • 10 ^ 12 / ho'āo ai;

  • ke kiekie pae o hemoglobin - 240 g. / k;

  • huina erythrocyte (OOE) aku i 52%.

Mai ka helu o ka ula koko keena,ʻaʻole hiki ke ho omaulia ma ka kumu o ka luna, e kaha nā loina, hoʻohana 'ia no ke ana ana radionuclideʻike. Inā ka nuipa o ka ula koko keena, ua oi aku ma mua o 36 ml / kg i ka na kanaka a me 32 ml / kg i loko o nā wāhine, ka mea reliably Hōʻike i ke alo o Vakeza maʻi.

I ka polycythemia paa ia i ka morphology oʻulaʻula koko keena, oa ka mea, e ole hoʻololi i kā lākou maʻamau shape a me ka nui. Eia naʻe, a me ke kūpono 'ana o ka hālāwai hoʻolohe anaemia, e excessive kahe ana ke koko a me ka hele pinepine mai kahe ana ke koko ae nānā mau microcytosis (ho'ēmi i kā ulaula i ke koko aeee).

Polycythemia: lapaʻau

Good pākōlea hopena i bloodletting. Ua pono pule e wehe 200-300 ml o ke koko like loa me ka nui o OOE e e haule i ka makemake nui. Inā loaʻa i contraindications no bloodletting, Hoʻihoʻi 'ia mai i ka pakeneka o ka ulaula i ke koko aeee hoi e hiki no ka lilo ana o ke koko, dilution ma hohua mai i ka wai a hapa (macromolecular pāʻoihana ka lawelaweia ana intravenously).

It E e kaʻikaʻiʻia ma ka manaʻo iʻano pinepine kahe ana ke koko hiki aku ai i ke kūpono 'ana o ka hao deficiency anaemia ma a ma laila nō e like symptoms a me ka mahuahua ma ka platelet helu.

Me keia maʻi like polycythemia, lapaʻau pono kaʻaeʻana me kekahi mauʻai. ? Aeiiaiaiaaia e kaupalena hokii o ka ai a me ka iʻa me nā huahana, e like me ka mea, iloko o ka kiʻekiʻe nui o ke kumuʻiʻo, stimulates ka ha awina o ke koko. Oe hoi e haawi mai i ka momomaʻai. Naʻokoko ka poʻea pau i ke kūpono 'ana o ke atherosclerosis, ma o na la thrombi, i ka nui mea, a no laila, e hanaʻia i loko o kanaka e loaa ana mai ka polycythemia.

A me keia ano maʻi,? Aeiiaiaiaaia e hāʻawi koho i ka haleʻuwī waiū a me ka mea kanu me nā huahana, a me ka palena physical ha awina.

No hoi, ina diagnosed like "polycythemia", lapaʻau i nā chemotherapy. Pili ka mea, ma ke kiekie thrombocytosis a me ka wi maneo. Nō kāu, keia "cytoreductive hope paha" ( "Hydroxycarbamide" hoʻomākaukau).

A nei, i mea e uhi iwi ka lolo ka pahu kui o radioactive isotopes hoʻohana (nō kāu, phosphorus-32). I kēia lā, increasingly oukou hoole ana i na lapaau no ka mea, o ka mea kiʻekiʻe uku o leukemic hou '.

Ke Inc i komo ai i ka ka pahu kui o interferon ma ka iapaau ana o ka haumāna thrombocytosis hoʻohana lāʻau ' "Anagrelide".

Ma keia maʻi ua kākaʻikahi hana iwi lolo transplantation, mai polycythemia - he maʻi i mea ole ona e, aka, o ka papa, kūpono ka lapaau a me ka ikaika aku ka mālamaʻana.

Polycythemia i loko o nā pēpē i

Polycythemia - he pathology, na symptoms o i hiki ke loaʻa i loko o nā pēpē. Ka maʻi o ke kino o ka pane ana i ka hoolilo hypoxia hunahuna, a hiki hoʻonāukiuki placental insufficiency. kamaiki i ke kino, e paʻipaʻi hypoxia hoʻomaka e synthesize i ka nui helu o ka ula koko keena.

'Olu o naehana hoʻoponopono, ke keiki e hoʻomōhala a me ka polycythemia vera. Oia ka pilikia i pakahi aku la ia ua hoopili i hooleiiaʻi mawaho mau māhoe'anetelope lāua.

Polycythemia i loko o ke keiki e hoʻomōhala ana i loko o ka mua mau pule o ke ola, ka mea, o ka mea mua hoikeana o ka mahuahua ma ka hematocrit (60%), a me ka nui māhuahua ma ka hemoglobin.

Neonatal polycythemia he mau kahua o ka hoʻonaʻauao o ka pele: ka loiloi mua, ke kahua poliferatsii a me ka exhaustion. Pokole kakau ia.

I ka loiloi mua ke kahua o ka maʻi iʻaneʻane ole i kekahi lapaʻau hoikeana. Polycythemia hōʻike mea hiki wale ke keiki ma kēia kahua ma ka haʻawina o kaʻike ākea koko: hematocrit, hemoglobin 'ilikai a me kaʻulaʻula koko keena.

Ma ka anu u poliferatsii e hoʻomōhala ana i ka hooakea aku i kou ake a me spleen. Pletoricheskie malamaʻike manaʻo: ka ili loaʻa kekahi ano "pletoricheskiʻulaʻula" hue, i ke keiki hōʻike ka iini wā i hoopa mai ai i ka ili. Pletorichesky maʻi pale complemented thrombosis. Ka Ikepili o ka malama loli i loko o ka helu o kaʻulaʻula koko keena, platelets a me leukocyte loli. e māhuahua ai nā hoailona o ke koko aeee i kekahi, ua kapaia ia ka kŰia "panmieloza".

I Wa depletion ua wehewehe aku ma ka nui ke kaupaonaʻana poho, asthenia a me ka exhaustion.

No ka keiki lapaʻau loli e like loa kaumaha, a hiki hoʻonāukiuki irreversible loli, a mahope make. Polycythemia paha e kaʻaihue o ka ulu i kekahiʻano o keʻokeʻo koko aeee i nā kuleana no ke kino o ka'ōnaehana paleʻea kahua. E like me ia i kaʻilihune, ka mea keiki e hoʻomōhala ana i ka wī nā mea palahēhē o ka mea koʻohune ke ano maoli, alakaʻi o ultimately, e make ia.

heluhelu i kēia 'atikala ma hope, oe e aʻo hou aku e pili ana i kēia maʻi like polycythemia. Symptoms a me ka hana i noʻonoʻoʻia e mākou i ka au mamuli i hiki. Mākou manaʻolana i ka 'ike i haawiia mai e e pono ia oe. E malama no oe ia oe iho, a noho ola!

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