Ola kino, Maʻi a me nā kūlana
Aplasia (agenesis) hakuʻala: 'ehaʻeha ka, symptoms a me ka hana hiʻona
Me ka excretory'ōnaehana ia mea hiki ole e hoi i noonoo ai i ka hana ana o ke kanaka kino. Kekahi o kona eiiiiiaiou i nā puʻupaʻa. Kēia hui kaulua hui, ke kumu hana o ka i mea i loko o ke kinowai loko a me ka wai wailana hehee wale. Ua Ua i pili 'ole i loko o ka pūnao a me ka rula o kaʻakika-kona'ākilikai koena. Ke kino Ua loa ola kanaka ma laila nō nā puʻupaʻaʻelua. Ma 2,5% o nā pēpē i nā hewa. A eia nae pohihihi, akā, i loaʻa i'āno'ē hakuʻala.
He aha ka aplasia (agenesis) hakuʻala?
Kumu, symptoms a me nā nohoʻana no nā mea pohihihi keia maʻi e e kūkā mai ma lalo nei. Mua, e pono e maopopo ka mea i manaoia ma kēia mau hua'ōlelo.
Ma nā 'inikua maopopo kahi pukeʻoe ke loaʻa i ka hui o ka manaÿo elua o "aplasia" a me ka "agenesis". Ua loaʻa kekahi hoʻokaʻawale iki ma waena o lākou? Agenesis - he piha nele i o kekahi a me nā o na puupaa elua. Kēia pathology He innate. Ma ka paena o ka nalowale kino mea,ʻaʻoleʻo ia i nā kumu o kaʻaʻa puʻuwai'aʻaʻa. Aplasia - he kŰia ma i loko o ka retroperitoneal lua mea wale ili aku ai o connective'aʻaʻa. Ma na olelo e ae, ia mea underdeveloped hakuʻala mea,ʻaʻole hiki ke hana kona kuleana pili i.
Ma lapaʻau hana, ka mea, aole ia i mea iʻano o ka maʻi i loaʻa i loko o nā keiki. A ma ka mea, a ma kekahi hihia, he piha kino i kahi e. Single maʻi 'ikepili helu i hoakaka ia. Ua ua ikeia eʻaʻa puʻuwai abnormalities hoike no ma kahi o 7-11% o nā pathologies a pau o ka genitourinary nenoaiu.
mōʻaukala 'ike
ʻaʻa puʻuwai agenesis ua, ua ikeia e ke kanaka, mai ka manawa kahiko o ka'āina. Kēia maʻi, a hiki i hoike ia Aristotle ma kana mau palapala. He ua kūkākūkāʻia ia ina he holoholona me ka naʻau ke ole, me nā puʻupaʻa a spleen - loa. Ma ka pakebona, keia pilikia i hoihoi i loko o ke nä känaka 'epekema Aaeuaeeneei Manuela Vezaly. I ka 1928, i ka Soviet kauka Sokolov 'ia paha, e kuhikuhi i kona prevalence i waena o ka heluna kanaka. Mai laila, noiʻi i ua anao? Aou kekahi mau pepa aplasia (agenesis), kela mea keia mea o ka a i kona mau lapaʻau kiʻi, a me ka olelo wanana a.
ano agenesis
Aia i kekahi mau Mea Maluna o ka maʻi. I ka papa kuhikuhiE hoomaopopo i ka maʻi ma luna o ka helu o ke kino.
- Akau-kapakahiʻaʻa puʻuwai agenesis (kuhi ICD-10 - Q60.0). Kēia palapala no ka kāna hana ua loa olelo diagnosed i loko o nā wāhine. IeAUPIIe, IAa IO mai ka hanau mua hakuʻala mea oi loa kūlana. Ua Ua Aia ma lalo o ka hema, a ua manaoia emi lawe lima. Ma ka hapanui o hoopii, a pau o na mana kuhi hui kaulua hui, a me ke kanaka uaʻaʻoleʻike piʻi nui discomfort.
- Haʻalele-mńlualua hakuʻala agenesis. Kēia palapala o ka maʻi mea pohihihi keia, a hāpai paakiki lawa. Ka'ākau hakuʻala Ua emi functionality. Ua ua i hakuloli ia ka uku hana.
Mākou E hoi noonooʻeluaʻaoʻao agenesis. No kēiaʻano o ka maʻi ua wehewehe aku ma ka wa e kaawale aku o nā ana o na kino elua. Ma lalo o kona mau keiki kākaʻikahi ola. Ma hope o ka hanau ka mea, koke pono transplants. He aha meaʻeluaʻaoʻaoʻaʻa puʻuwai agenesis kuhi? ICD 10 nā ka pathology ma lalo o kuhi Q60.1.
'ano apau loa aplasia
Kēiaʻaʻa puʻuwai anomaly mea wale nō hoʻokahi-kapakahi. Ke pathological kaʻina hiki ke haawi wale n? Ma ka hema a me ka akauʻaoʻao kino. Pela hakuʻala fibrous'aʻaʻa ana na poe ma rudimentary palapala, akā, me ka pelvis, ducts a me glomeruli.
Nā kumu o ka kāna hana
Aia mea i kona manaʻo ma e pili ana i na kumu o kaʻaʻa puʻuwai agenesis i loko o nā pēpē i hakuʻole. Kauka i kāheaʻia kekahi mau wahi o Hawaii. Kekahi ike i ka loulou pathologies me ka aaiaoe predisposition. 'Ē aʻe hoole i kēia mea.
Lōʻihi-manawa study o ka maʻi, a me nā haʻawina lehulehu ua 'ae' ia e hōʻike ana i ka helu o nā kumumea, i ke alo o ka mea maoli i ka pahiki o kona hanana. Aplasia a fetal hakuʻala agenesis hiki i loko o nā kēia hihia.
- Maʻi alcoholism, ka hoʻohana 'ana o ka waiʻona i hāpai keiki.
- Mimikō i loko o ka wā e hiki mai makuwahine.
- A mea hoʻomaʻi / infectious maʻi i loko o ka trimester mua.
- Ke kipi 'ana o ka ai' o ka wahine no no 9 mahina.
Nā puʻupaʻa hoʻomaka e hana i loko o ka fetus, mai ka hebedoma 5th o kona ola i loko o ka opu. Kēia kaʻina hana mau ma ka hāpai keiki. Naʻe, i ka noho pilikia loa i ka 1st a me 2nd trimesters. I keia manawa, i ka likelihood o ka ulu maʻi, nae i ka hopena o ka noho lakou malaila aʻe, ia mea he kiʻekiʻe.
Ka pono lapaʻau kiʻi
Aplasia a agenesis o ka hakuʻala i e ka lōʻihi loa manawa 'aʻole i hōʻike aʻe. Kekahi makuwahine i hāpai keiki e, mai hele i ka US, a ma hope o ka nānā aku ana o ke keiki ua malama ole kālailai. E like me ka hopena, kanaka i ole i ka ike o na ola pilikia. He aoiaʻi oe i ka ka meaʻawaʻawa loaʻike, ma luna o ka makahiki. E like me ka rula, oiai e oaeouee? Examinations ma kula a ma ka hana. Ma keia hihia, he olakino hakuʻala lawe ma i ka 75% o ka mana o ka nalowale a poorly functioning hui,. Nolaila, kekahi 'aʻole i haha aku i kekahi discomfort.
I kekahi manawa,ʻaʻa puʻuwai anomaly hoʻomaka e hōʻike i ke keiki i loko o nā lā mua o ke ola. Mawaena o ka papa kuhikuhiE symptoms o ka pathology kauka kaʻawale.
- kela lehalehu t mā (puffiness, ka laula, a me ka ihu);
- he nui helu o wrinkles ma luna o ke kino;
- hoʻopuni mai ka'ōpū;
- haahaa kulana o ka pepeiao;
- deformation o ka lalo lala;
- offset olelo o kekahi kūloko ma nā loko.
I ka mea, ua diagnosedʻaʻa puʻuwai agenesis o ke keiki, i ka maʻi ua ana pu ma'āno'ē ulu o reproductive nā loko. No ka laʻana, na kaikamahine hōʻike elua-pepeiaohao uterus, vaginal atresia. Nā keiki i loaʻa i ka wa e kaawale aku o vas deferens. I ka wā e hiki mai, ua pilikia hiki ke huikau ma ka impotence a hiki infertility.
ki ina hana like o kaʻike,
mau i ka makua i kaʻike, "ʻaʻa puʻuwai agenesis" kīnā o ke kino. Eia naʻe, e pono mua kekahi, i ka hulina ninaninau. Iloko o ke anaina i ke kauka 'ohi i ka hoʻomanawanui i ka' inikua mōʻaukala, Pilikanaka kona hereditary predisposition. nā ano o ka hana noiʻi i e pono ai e hōʻoia i ka ka muaʻike,:
- 'Amelika.
- Urography me ka Akä naÿe hope paha;
- ʻaʻa puʻuwai angiography;
- HI.
E hoʻoholo i ka wa e kaawale aku ai hakuʻala fetal hypoplasia hiki ma ultrasound. Ua i ka mea mua loiloi ao, a ua häʻawi mai ai i ka la pule 12-14, ka hoʻomalu ke hoopaa i ka pathology. Ma hope o ia, o ka wahine pono ia ka mea hou loiloi no ka pili malformations.
'inikua therapies
Ka wale ano o ka maʻi, a maoli ho i ka pilikia e ola - ia mea heʻeluaʻaoʻaoʻaʻa puʻuwai agenesis. Muli o kona kulana pinepine make nō ka hua me kēiaʻike, i loko o ka opu a ma ka hanau ana. Nō hoʻi, i ka pahiki o ka make i loko o ka mua mau lā o ke ola ana Ua kiʻekiʻe no iʻaʻa puʻuwai ole.
Ma ka hooulu ana o perinatal lapaau i keia la i ka manawa e hoola i ke keiki me keia pathology. E hana i kēia, ma ka hora mua ma hope o ka hānau he hana e transplant nā loko, a laila, e maʻamau hemodialysis. Kēiaʻaoʻao o ka hana maikaʻi i ka maʻi mea maoli, a ua hoʻohana 'ia i loko o ka hana pono i ka nui' inikua-oaio? A. Eia naʻe, initially E e hoʻonohonoho hoʻokēʻai palena pauʻike, a me ka neʻe 'ē aʻe malformations o ka urinary nenoaiu.
Unilateralʻaʻa puʻuwai agenesis i ka maikaʻi prognosis. Inā ka hoʻomanawanui no ka maʻi ua i huikau ma kaʻawaʻawa loa symptoms, ia mea nui i ka makahiki checkups, a lawe i ka mea e ho'āʻo ai. Ua mea i pono, e mālama ana i ke olakino hakuʻala. Piha koi e haawi aku i ka hana maikaʻi kauka. E like me ka rula, e nā kaʻaeʻana me kaʻai a me ke koe o ka huʻi a me ka palemo iho ai, e haawi ana i inoʻano.
Aplasia i pelaʻia. Eia naʻe, hiki ole ke hana me kāohi koi, e hooikaika i ka'ōnaehana paleʻea nenoaiu. Oe Pono eʻai'ākau, pale aku infectious a me ka mea hoʻomaʻi maʻi. Ua ua i pono, e haawi i mea hoounauna.
I loa pathological kaʻina e koi dialysis paha hoi he hui, transplant. Ma nā mea a pau nā hihia, Inc E e pākahi kā i ke ano o ka maʻi a me ka nohona ma lapaʻau kiʻi.
aoao e pale aku
Aplasia a me ka agenesis hakuʻala nā loina ma ICD-10 iʻokoʻa. Eia naʻe, nā o kēia mau maʻi i mea e hopohopo nei i waena o prospective makua. Ua mea hiki, e pale aku ia lakou mai ka hana?
Inā e hookaawale ia i ka aaiaoe predisposition i illnesses, ke kāohi ana i na mea kupono. A hiki ma ka hoʻolālā ke kahua, ka expectant makuahine pono hoʻomaka e kanaka hoʻoponopono i ko lakou ola (ai pono, haalele inoʻano, komo i loko o haʻuki hiki). Na koi e e hahai aku ma hope o ka holomua hapai ana bebe.
Inā 'oe hiki ole pale ia i ka hooulu ana o ka pathology, ia mea pono, e lawe ana i kona hoʻopau. A hiki aku ka mea, heʻeluaʻaoʻao agenesis symmetrical fetal developmental 'ole, oligohydramnios. I Ina o ka loaʻaʻana o nā anomalies mua 22 pule o ka gestation ua paipaiʻia kona hoopau wale ma 'inikua kai. A hiki ka wahine mai ia i hoole ai, hoʻohana makeʻe kulana obstetric nā kaʻa mokulele. Ua mea waiwai 'ana i kumumanaʻo i loko o ka wa e kaawale aku o unilateral hakuʻala hiki ia i ka piha ola. Oe Pono wale kēlā wā i kēia wā undergo kāohi ponopono-ae la a me examinations.
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