He aha ka Ollier maʻi. Ollier ka maʻi:ʻike, a me ka lapaʻau

Oe makemake manaʻo i kāu uuku keiki wāwae a me na mea kaua e ulu lohi? Paha ia i Ollier maʻi. He He maʻi i loko i loaʻa nō abnormalities o ka iwi? Acaeoey o ka iwi, i mea, kona dysplasia. Other inoa i olelo ia lakou i na mai - mau chondromatosis iwi, unilateral paha chondromatosis diskhondroplaziya iwi. Kona papa inoa maʻi ua ma ka aoao o Lyons surgeon Olier. I ka maʻi, ua loaa, a ho'ākāka 'ia ma ka hoʻohana' ana o ka X-kukuna i ka 1899.

He aha ka ka mai Ollier

Kēia maʻi pili i abnormalities o ka pokou iwi, a e pili ana i na maʻi, me pono-ike i na mea he nui makuahine keiki hip-dysplasia.

Ka maʻi ana hoike mai ai ia i ka wā kamaliʻi, no ka mea, o ka mea i mua manaʻo i keia keiki ka maʻi. Ua ua manawa ho'āʻo i ka pathology ke e kona Debut ma mākua (symptoms ke ana a hiki i ka makahiki huahelu 20-40 makahiki). He He congenital abnormality, akā, ua loaʻa kekahi manawa hope - ma ke kakahiaka kamaliʻi a ma ka adolescence -ʻo ia, i ka manawa o ka ulu mālama nui, ka wā e lilo ka nohoaliʻi deformation o ka iwi a me / ai'āno'ē kūpono 'ana o na lima a me nā wāwae.

Ollier ka maʻi i loko o ka metaphyses o lōʻihi omo iwi o ka lala ikea ka ulu o ke o ka cartilage. Mai e hoʻomōhala ana iʻano nui i loko o ka iwi, cartilage, a me ka ami o na lima a me na wawae, pakahi aku la ia ma na wawae a me na lima, e like me ia ma ka pelvis, akā, ka mea, ua loaʻa i loko o ka iwi, a me ka sternum iwipoo.

Ka ulu o ke a enhondromy e ka pā, ahu iho o ka iwi lahilahi, a brittle. I mea, ia mea he benignʻeho i hiki hoʻomōhala i loko o malignant (e like me, chondrosarcoma). Mea pōmaikaʻi, keia hana loa kākaʻikahi.

Ma puberty ka ulu o ke stabilize a UAIAaIN ma ka iwi.

Penei, Ollier maʻi - kaumaha hereditary maʻi, calcification o ka cartilaginous iwi i loko o ka mea no hoi ia lŘlŘ a me ka hanaʻia naʻe metaphyses (iwi lōʻihi o ka'ā'ī). Ke kumu no kona hanana mea nō IKE OLE IA. Ma kekahi mau hihia, ia mea he autosomal Hoʻohaku aaiaoe külana.

Similar e diskhondroplaziey na mai i pohihihi keia syndromes maffucci a me Proteus. Ma mua, 'Aʻohe wai iaʻu, mai benign ka ulu o ke cartilage a me skeletal deformities,ʻili i hana hemangioma -ʻula mau kiko ole kinona, oia no na moku koko. Ma ka lua o ka ulu benign hikoko i loko o nā wahi likeʻole o ke kino.

Wai ua loli ana e ka maʻi

Mua ia i manaʻo i nā iwi chondromatosis pohihihi keia. Aka, ano, i ka wa a ka X-Ray keia hookolokolo ana ua lawe mai kaiāulu lawa, e huli mai ia ia mea,ʻaʻole he rarity. Inā 20 makahiki aku nei, ka mea i ho'ākāka 'ia ma 30 hihia i ka mea, i kēia manawa pāpālua ihola lākou i na mea he nui.

E hoʻoholo i ka kiko'ī hookahi ana mea hiki ole ina ka hanau i ole ia he mau hōʻeuʻeu study hoʻohana X-kukuna, o ka oi aku i loko o kakahiaka kamaliʻi a me ka fetal? Acaeoey, ia, ma ka mea, ma laila Ollier maʻi. Ka maʻi mea, ma ke ala, na kaikamahine hōʻike aneane elua manawa hou ma mua o nā keikikāne pinepine.

symptoms

Not i hala i ka hoailona o ka maʻi, nā mākua e e wary inā he keiki:

• mai hoʻokaʻulua aku i loko o ka ulu ana o kekahi mau wahi o na lala /ʻaoʻao;
• na hiohiona asymmetry a me ka hua'ōleloʻo loko o ia mau mea;
• ae nānā mau lameness;
• he mea misalignment o na pelvis;
• keia curvature o na ami o ka valgus a varus type.

A pau kēia mau kumumea e ka mea e hiki ai, e kuhi ana i ke keiki Ollier maʻi.

Ka maʻi mea i mau koke akaka no i hanau, akā, i ka makahiki o ka 1-4 makahiki, oe, e hai ana i ke keiki i ke kua'āina ma mua o manaʻo, mahuahua na wawae a me na lima. 'O kēia ka papa kuhikuhiE symptom o ka maʻi, i hiki ole ke AOON. Ke koena o ke keiki ua ulu maʻamau, hoʻowahāwahā i ka mea i ka mea, i diagnosed me "Ollier ka maʻi."

Diskhondroplaziya loa pinepine e loli ai kekahi lala, akā naʻe, aia no na hihia o ka make a elua. Inā ka maʻi i hoopa ia, i ke keiki e e ulu ana malalo ma muli o kā lākou i ka hua'ōleloʻo. No ikaika stunted iwi ina ka pathological kaʻina hoʻomaka loa kakahiaka. Deformation ke hoomau aku painfully lohi holomua. O ka papa, waiū i ka maʻi, lilo pōkole, pūhaka, hoʻololi ana, 'lameness ua malamaia. Aia paha e kekahi varus paha valgus deformity o ke kuli (emi pinepine - ka proximal hope o ka femur a wāwae), scoliosis o ka spine. Muscle atrophy ma keia maʻi mea,ʻaʻole i loaʻa.

Big loli mea malalo iho a hiki i ka phalanx, metatarsal, a, ma kekahi hihia, na metacarpals. Lakou hoopokole, kikooia aku, clumsy a me ka cartilage pihaʻi me na mea he nui hoʻomāʻikeʻike wale nō.

Ollier ka maʻi paha e fracture like me ka hopena o ka maʻi e hoʻomohala i ka iwi hewa. Eia naʻe, fractures pinepine seamlessly ulu.

Comorbidities

Diskhondroplaziyu hiki pu lesions o nā nā loko, eia nae nā maʻi hoʻomōhala mau mea ole. Ma mau, ma ka opiopio kaikamahine me Ollier ka maʻi e ana teratoma o ka ovary a me ka endocrine kāna hana, a me ka wi, a me ke kakahiaka nui menstruation a precocious puberty hōʻeleu i ossification.

Eia naʻe, ua hoi aku ka hooulu ana i ka maʻamau ma ka wehe 'ana i ka ovaryʻeho.

lapaʻau '

E kuhikuhi i Ollier ka maʻi, ia mea mua e pono ia e ka roentgen. Aia E hoi e ka iwi biopsy a me kaʻume mākenēki resonance kiʻi. I ka loaʻaʻana o ka maʻi, nā mea maʻi e noi mai ana regular ponopono-ae la ma kekahi kauka, ina he pono, e koke hōʻike i ka malignant hou 'ana i chondrosarcoma.

palena pauʻike,

Palena pauʻike, o Ollier ka maʻi, ma ka mea,ʻaʻole e pono ma hope o ka X-Ray, no ka mea, ke kiʻi loa kekahi chondromatosis. Eia naʻe, kēlā me kēia hihia o kanaka, akā, i ke kaʻina o nā ola symptomsʻaneʻane hou, no laila, pono e noho mai kauka i ka helu o ke ano like ka maʻi.

Roentgen eliminates atypical Chondrodystrophy, hemihypertrophy a iwi atrophy, rachitic deformation a me kekahi mau maʻi'ē aʻe. Nō hoʻi, ma muli o ka X-kukuna, ka mea, ua hoʻokoe 'Recklinghausen maʻi, i IeAUPIIe, IAa IO hiki ke pioloke Ollier maʻi. Na ka papa kuhikuhiE rula - pono, e hana i ka m-Ray ka iwi a pau, aole i ka hapa o ka ia.

lapaʻau Nā Kūlana

Diskhondroplaziya ma ka manawa, Eia naʻe,ʻaʻohe ka naauao ano o ka nohoʻana. Akä naÿe, no kekahi laʻana, na maʻi like Hip dysplasia, chondromatosis hana wale maʻoki lāʻau lapaʻau? Iaea o deformation. Ma kekahi mau hihia, e hōʻike iʻimi hoʻopunipuni hip-hope. Ke koena o ka lapaau ana i ke ahonui e loaa, - symptomatic a me ka hope.

ʻoki lāʻau lapaʻau 'uao ua hōʻikeʻano nui no nā mākua, mahope mai, e like me ke kālā no loina, ka wāʻoki lāʻau lapaʻau? Iaea ma ke kula makahiki pahuhopu nei hualoaʻa i, ua loaa ia, a' o ia hoʻi i ka ano o kaʻoki lāʻau lapaʻau lapaʻau ua wale nō i hanaʻia i deformation, akā,ʻaʻole hōʻeuʻeu. Eia naʻe, ma ka loa nā palapū hikiʻoki kino no na keiki, o ka oi aku ka wā e hele mai ai i ka manamana lima, a me ka nui loa i ka nānaina ma Ollier maʻi.

Ka maʻi pono ka malama ana hui a me ka iwi: e hoomanawanui i hōʻike 'ia ua hoʻokomoʻia orthopedic kamaa, ka hoʻohana' ana o orthopedic koo aku a me nā manaʻo no ka hoʻopunipuni ami. Nā mea maʻi e komo 'ia ua hōʻike hewa no keia pathology lapaau a me ka hoʻokō haʻuki eiiieaena.

Pono keia mau mea me gymnastics a me nā kino ma kūikawā simulators. Ua kōkua e hoihoi Muscle kamaʻilio a me ka hoʻoikaika i nā ligaments.

Outlook

E like me ka noiʻi, ka hapanui pinepine ma puberty, cartilage UAIAaIN ma ka iwi (malia o ia ka ke kumu i ka makua hihia o ka maʻi i 'akomi i loa kākaʻikahi). Naʻe, ke kēla mea emi o raduzhen i loko o na keiki opiopio: deformation, albeit lohi, akā, ua holo pono. 'O kēia ka mea pilikia loa Ollier maʻi.

Ka maʻi hoike mai ai ia ia iho, no laila, pākahi i loko o kēlā me kēia hihia, i ka nohona ma prognosis mea hiki ole i ka Loiloi i unambiguously. Ka wā mau lesions ia mea oi maikaʻi ma mua i loko o ka hihia o hookahi IIeEeAIEUIeXAIIUE nā loli. Single deformation hiki aku ai i ka hua'ōleloʻo o kekahi o na lala a me keia wahi aku, ma kā lākou mau asymmetry, o ka oi aku ka wā e hele mai ai i na keiki uuku. A he mea hiki ole ke koho. ¶ A i loko o ke kakahiaka 'ana o ka maʻi' aʻai maoli i ka pilikia o kekahi mau deformities o ka manamanalima.

Hou 'i loko o chondrosarcoma

I loko nō o ka mea i malignant hou 'ma ka manao - chondrosarcoma -' ole e hana pinepine, aole nae he mea i ka manawa o ka ulu maʻi 'aʻai. Ka hapanui o kēia ka hana i loko o adolescence, ina ka helu o kaʻikena noiʻi hōʻike i ka mea hiki ke hiki nui hope. No ia kumu, ua paipaiʻia nā mea maʻi diskhondroplaziey regular kona kūkā me ke kauka a me ka 'inikua examinations.