Ola kino, Ka noʻonoʻo '
Lennox-Gastaut maʻi pale (epilepsy)
Lennox-Gastaut maʻi pale - heʻano o ka epilepsy (myoclonic-astatic). Oia maʻiʻano komo ai i ka hoʻohui pū 'ia o ka tonic a me atonic kāʻili' ana, atypical wa e kaawale aku ke kāʻili 'ana, hoolohi noʻonoʻo kūpono' ana i loko o na kamalii uuku. No ka mea manawa mua i ka maʻi ke hoike mai ai ia ia iho i loko o na keiki, mai kekahi i ka elima,ʻano nui no nā keikikāne.
Kēia maʻi ana e hoʻomōhala ana i like me ka hopena hoololiia no ka noho 'ana kamaliʻi neurological maʻi, a hoʻomaka me kekahi ulia e like i loko o ke keiki. Ma hope o kekahi manawa, he mau convulsions, ke kāʻili 'ana, ka hoike kali koʻu noʻonoʻo kūpono' ana, a ua hoemiia akamai.
Ke kiʻekiʻe, a me ka ulu ana o ke keiki, i ke ano o ke kāʻili 'loli aʻe. Hāʻule UAIAaIN ma anoe, secondarily generalized, luna 'ino o ka epilepsy.
No ka mea, o ka mea ua hoike mai Lennox-Gastaut maʻi pale
E maopopo i nā kumu o kēia maʻi pale ka pilikia lawa, akā, i ka lā iʻikeʻia e ka nui poʻe.
- Ke anomaly o ka lolo? Acaeoey.
- Loa nā mea palahēhē (meningitis, encephalitis, rubella).
- Aaiaoe pathological lolo maʻi (CNS, metabolic maʻi, tuberculous sclerosis).
- keikiʻeha i ka hooholo ana o ka hanau Canal (hānau asphyxia, premature hanau, etc.).
- CNS eha ma ka perinatal au, e like me preterm e hānau ai a me ka asphyxia.
symptoms o PLGA
Lennox-Gastaut maʻi pale hiki keʻikeʻia ka loa nui symptom - no ke kāʻili 'ana. Children ka poe i diagnosed me "idiopathic epilepsy", pili pū kēia i kekahi mau ano o ka epilepsy (symptoms) :
- paroxysms o Hawaii;
- atonic kāʻili 'ana;
- atypical wa e kaawale aku;
- ka helehelena kāʻili 'ana;
- sternocleidomastoid cramps;
- myoclonic-astatic kāʻili 'ana;
- tonic kāʻili 'ana (IeAUPIIe, IAa IO hana ana i ka hiamoe nui);
- TC generalized ke kāʻili 'ana.
Nā mea maʻi i ka maʻi pale o Lennox-Gastaut no hoi i ke ano moku'āina o ka, nanea ana me ka pahee hoʻololi i loko o epilepsy, noʻonoʻo retardation, cognitive a me ke kanaka me kāna hana.
Diagnosing i ka maʻi pale LH
Koke ma hope o ka mua symptoms o ka maʻi e koke imi 'oihana kōkua, e kāhea aku i ka ambulance. Nō kāu, ua lawe maiʻike, o ka maʻi me ka hoʻohana 'ECG ma waena o ho'āhewa wale.
LH maʻi pale iapaau ana
Lennox-Gastaut maʻi pale ua ia me ka lapaʻauʻia, aʻoki lāʻau lapaʻau 'ana i kūpono. Iapaau ana me ka laau e hua maikaʻi i loko o nā hualoaʻa i hou aku 20% o ka hihia. Ma kaʻoki lāʻau lapaʻau iapaau ana ano no ke kāpaeʻana ulia kulu, ia mea mana, e oki i ke kino callosum (callosotomy). Nō hoʻi, ka hoʻohana 'ana i kauoha ai i ka stimulation o ka vagus nā aʻalolo a me ka wehe' ana o vascular hikoko a me malformations.
Naʻe, ka mea e e kaulana i ke kāʻili 'ano o kēia maʻi pale ka pinepine ole i ka hana; i loko o ka hopena ka mea, ke i ke hoʻomanawanui i ka loa a me ka nohona manaʻoʻike hopena. ʻaneʻane untreatable tonic kāʻili 'ana, a alakai ai i lalo akamai.
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