West maʻi pale

No ka mea manawa mua malihini infantile spasms i ua hōʻikeʻia e West i loko o ka 1841st. A laila, ka mea, ua i ka ninau o kana keiki iho. Pakahi aku la ia ua hoʻokoʻikoʻiʻia noke i holopono nō psychomotor symptoms ma. I ka maʻi ua kuhi maʻi.

West maʻi pale komo pū triad ano symptoms - repetitive moʻo o spasms, psychomotor retardation, hookahua loli (paroxysmal) ma luna o EEG. Omaka ke kiʻekiʻe, ka mea mua symptoms e pono ana a hiki i ola na keiki mua, aole nae ana ike aku i ke kāʻei kua o ka loa psychomotor ke kali ole. More, he pono ole i na keiki eha i ka eono mahina, akā, he mea hiki i ka maʻi ma hope (i ai i eha makahiki). Boys olohelohe ia lakou i ka maʻi hou.

Infantile spasms pele symmetrical,ʻeluaʻaoʻao, pōkole, me ka ulia contraction o Muscle pūʻulu. Ano ho'āhewa wale hilinaʻi nui ma luna o ka pūʻulu komo i loko o ke kaʻina (flexor, extensor). Cramps hiki e hohola iho la kekahi ma luna o nā mea a pau o nā nāʻiʻo a me ke kanaka ('ā'ī nāʻiʻo, i nā nāʻiʻo o ka abdomen). Olelo loaʻa hui spasms, i ukali ia e prevalence - flexor, a hiki rarer - ka extensor. Eia kekahi, aia no he spasm hilinaʻi nui ma luna o ka mau kulana o ke kino.

West maʻi pale pinepine kaʻoi loa flexor spasms hoomaopopo. Inā 'oe i ke komo abdominal nāʻiʻo-flexors, i ke kino ke ano laulā, e pelupelu ia ma ka hapalua. I ka wā o ka hoʻomau ana maluna palena, lima neʻe ua mālamaʻia neʻe iki-hookomo ana (ka mea nani i ke keiki ia ia iho i hoʻomaka e apo). Me ka komo o ka flexor nāʻiʻo o ka'ā'ī fits me kona hoʻomaka 'ana. Inā ka ke komo pū o nāʻiʻo o ka poohiwi kaei, i ke keiki me ia shrugs. Spasms ke kaupalena nistagmoidnymi ka neʻe 'ana a me jerking o ka'ōnohi a poʻopoʻo. Hiki a me ka ÷ naehana hanu ole. 'O kēia ka mua symptoms o epilepsy.

Ano o spasms o ka etiology, aole ia e hilinai nei, e like me ka mea e ae e wńnana i ka kūpono 'ana o ka maʻi. Naʻe, i ke kūlana hoʻokani ma ke alo o ka symmetry (asymmetry Hōʻike cortical lesion). e hooponoponoia ia mea, Asymmetric spasms, no ka laʻana, ke kīloi paʻewa-kēpau mau maka a me ke poo.

Spasms pele i hoʻomaka ai ma luna o ke ala 'ole e haule ana e hiamoe ana pēpē. Emi iho malalo o kekahi minuke wā mawaena therebetween. Ka nui, piʻi pū, a laila, emi. Kekahi alapine (frequency) - mai hookahi spasms a hiki i na haneri no ka lā. Ka mea hiki ke kena ae la ia e ka leo halulu a tactile.

Hope e hele mai ana au cramps hoemiia reactivity. haule Kids ka mea ua hele, hiki koke (kulu ho'āhewa wale).

West maʻi pale ua manaoia e ia, i ka loa e like me ka ano o epileptic encephalopathy alakai i cognitive hoʻopilikia. Ma Kāohi mea oleʻikepili.

West maʻi pale ia lŘlŘ ma muli o ia mau kumu. Asphyxia - ka loa, he pono ole. Eia hou, ka mea hiki ia he congenital abnormality o ka lolo, intracranial hemorrhage, a pela aku. I kekahi manawa, i ke kumu o ka maʻi hiki ole ke nānā '.

Inā kou kamaiki West maʻi pale, lapaʻau hoʻomaka koke. Oe ke koho i ka 'inikua Inc, a me ia mea e hiki ai i ua koi' uao, a me surgeons ka pathological konu ka mea wehe, Aia kahi e ma o ka lolo. Auwe, i ka manawa e hōʻike i kēia kikowaena 'aʻole i mau e hiki mai, a ma kekahi mau hihia, i ka wā' akomi i, he mea hiki ole ke kāpae i.

Inā ka lapaʻauʻia ua koi 'ia e hele i ka papa loaa he kūikawā, pākahi i koho antiepileptic ai'. Cessation o ke kāʻili 'ana e hoike mai ai i ka pomaikai o ka Inc, nae, i ka iapaau ana e e hoopomaikai io ia he umikumamalima (a me ka palena iki) mahina. Lapaʻau ka hoao ana paipai i ka hale hānai kalaia ana o ka maʻi i loko o 60% o nā keiki, ho'āhewa wale no ka i koe, Eia naʻe, e hana hou ia.

ʻIseraʻela kauka i aku nei au, no ka maʻi me ka cryptogenic palapala prognosis mea nui maikaʻi. Mālama nui malama pana ho'āhewa wale, ke keiki "outgrow" maʻi pale, developmental kali hou aku; ua like hoʻonaʻauao nā pāʻani. Ka wā symptomatic ano o ka ino prognosis. Inā mākou e mālama i ka huki aku ho'āhewa wale, a hoʻopau i ke kumu o ka hoouka kaua o ka maʻi (malformation, hikoko, cysts), e hoololi i ka paʻewa noho kiʻekiʻe.