Ola kinoMaʻi a me nā kūlana

Darier ka maʻi: mea, lalau mai, symptoms, lapaʻau

Ka hapa nui o na kanaka o kekahi mau mea koe o ko lākou mau makua. Kekahi loaʻa nā maka uliuli o ka Pope, ka mea 'ē aʻe - lauoho chic makuwahine. O ka papa, i kekahi manawa hope versa. Eia naʻe, ua pau ulu i hoihoi 'hopena hili nā'ōewe o ko mākou pili hoahanau. Loa pinepine, me ka nui maka, curly ka lauoho a me nā wāwae lōʻihi, nā mākua e hāʻawi aku kā lākou mau keiki i ka lākou a okoa ka maʻi. Lakou hana i kēia,ʻaʻole ma ka mea, e like me kou 'ae' ana iho. Pathology hiki ole i hoʻomaka ai ma ke ola, akā, oi pinepine i ke kulana mea okoa. A kanaka i ka mea pani o ka ohana illnesses a me ka maʻi puʻuwai. I kekahi o kēia mau "makana" o Darier maʻi. He aha ka mea? He aha ke kumu keia pathology?

kekahi mau 'ike

Ma lalo o Darier ka maʻi pili i ka hereditary dermatosis hoike aku lapuwale ia i loko o ka palapala o ka nodules mea eleele a me ka eleele. Ka mea, heʻohana-hoʻokino, a uhi me ka manoanoa crusts. Nodules IIeEeAIEUIeXAIIUE ma luna o ke kino pā mai no ka ahakanaka, a hana i nā hua eha. Ke kaumaha ma muli o ka wahi o ka lesions a me kā lākou mau helehelena, Darier ka maʻi ua maheleia i eha 'ano apau loa.

  • IIeEeAIEUIeXAIIUE. Wehewehe aku ma ka laina hoʻoponoponoʻana o Kamehameha o na ioauoa o i uhi wale i kaupalena 'mau mea o ke kino.
  • Panina. Lapuwale ia puleʻAmelika, IIeEeAIEUIeXAIIUE ma ke poo, a me ka pahu pepeiao.
  • Kaʻawale. A me ka maʻamau nodules ikeia polyhedral papules like warts. Nō kāu, nō ka mea, ma ka hope o na lima a me na wawae.
  • Vesicular-bullous. Kēia palapala no ka maʻi ka loa pohihihi keia. Ua Ua wehewehe aku e mau lesions me ka aniani moakaka huna. ikeia ka mea, ma kaʻaoʻao o ka ai, i loko o ka wahi o ka nui ili pā.

N lesions papules i diagnosed i loko o nā mea maʻi ma waena o nā makahiki o ka ewalu i umikumamalima makahiki. Makua maʻi e pepehi iho at kākaʻikahi.

Nā kumu o ka maʻi

I ka papa kuhikuhiE kumu o keia maʻi o ke alo o'āno'ē'ōewe, a me ka nui kamepiula ololi - ili predisposition. E like me ka hopena, uaʻaʻole maopopo ke kemu wikamina A ma ke kino, ua hoemiia ka ha awina o kekahi nā'ūhū a me kiniki maʻiʻo ma na epidermis. Ke no ia mau hopena o kēia mau pathological keʻano o ka hanaʻana i ka 'aʻe' ana i keʻano papa hana o ka ili keratinization.

Inā makuahine a me Papai e nā moku halihali mokulele o ka'āno'ē'ōewe i loko o 50% o ka hoopii, no ka malamalama,ʻikea ke keiki me kaʻike, o "Darier ka maʻi." Naʻe, ina ka hoʻomanawanui iki mai na makua i hanau loa ola pēpē, keia pathology 'aʻole i bother i kona wā e hiki mai keiki. Ka maʻi 'aʻole i hiki ma airborne droplets' ole nā kiʻie.

lapaʻau kiʻi

Ke pathological kaʻina hoʻomaka me ka helehelena o ka palahalaha follicular nodules, a i ole ia i ike i papules. Lākou nui i ĸokoĸa ana nä pane mai 1 a 3 mm o. Papules uhi ia me ka paa pńpa o ka mea eleele ano. Ma lalo o ka mea, ma laila nō kaumaha i loko o ke kinona o ka funnel. Nodules i aia ma ka waha o ka lauoho follicles, i kekahi manawa, hiki aku ai i ka ulu ana o kekahi maʻi - folliculitis. No laila, ma mua e hoʻomaka ana lapaʻau mea pono e hoʻomaka i ka palena pauʻike.

Pele i hoʻonohonoho symmetrically'ālunu subclavian māhele 'āina a me ka flexor surfaces o na ami. Ma ka ili poo papule reminiscent warty scaly plaques me crusts. Ma hope o kā lākou wehe 'ana i loko o nā wahi o lesions ikeia foci o alopecia. E like me ka maʻi progresses ka mea, he hou rashes a kahiko merge i loko o ka hoʻokahi punahele.

Lapaʻau o keia hookolokolo ana

ʻike, o ka mea maʻi ua ma muli o ka lapaʻau kiʻi a me ka piha 'inikua mōʻaukala o ka hoʻomanawanui. Iloko o ka hookolokolo ana, ke kauka nana na symptoms o ka maʻi, mamua hihia o rashes iwaena o pili hoahanau. E hoʻokūpaʻa i ka maʻi ua ia he histological Ka Ikepili o ka ili biopsy. Ka palena pauʻike, ua lawe mai me kaʻohana pemphigus, papillomatosis a me seborrheic dermatitis.

Inc nā loina

Iapaau ana me keia maʻi ana hana ma luna o ka outpatient manawa. Ma exacerbation o ka pathological kaʻina 'ōili mai a nui lesions hoomanawanui pono hospitalization ma dermatological haukapila.

Ke hoomanawanui mea he symptomatic Inc. All nā mea maʻi i ole koe ia wikamina A i loko o ka palapala o ka moʻolelo a me intramuscular ka pahu kui. Laʻau heluna he pōpilikia pākahi, e lawe i ka mooolelo o ka hoʻomanawanui i ka makahiki. I ka papa o ka lapaʻau mea IeAUPIIe, IAa IO 3 mahina, a laila, e kaʻoluʻolu o a me 'oe i ka hana.

A maikaʻi result me Darier maʻi haawi Oe bato ma ka hoʻohui pū 'ia me ka palapala noi keratolytic mea poni. Ma ke alo o ka nui lesions,ʻoki lāʻau lapaʻau 'uao a electrocoagulation. A lohe o Darier ka maʻi ua pu ma ka hou ana o ka mea koʻohune maʻiʻaʻai, he antibiotic ua kuhikuhi.

I ka olelo wanana a me ka Kāohi

I ka maʻi ua ho'īli wale nō ma ka'āina hoʻoili. I mea no ke aha la e like me ka iniiaiie Kāohi poe akamai i waiho aku kūkā me ka geneticist i Leomakana hoʻoneʻe ai i loko o ka kokoke manawa i kō ai ke keiki. He oi loa oiaio o na makua, ka mea i loko o ka 'ohana i mua, ua diagnosed me Darier ka maʻi.

Ke lapaʻau i ho'ākāka 'ia ma luna, IeAUPIIe, IAa IO hōʻike maikai hopena. He nui nā mea maʻi e loaʻa ke kala ana ku nei no kekahi mau makahiki. Eia naʻe, kekahi e ole mai ana i ka piha ke ola.

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