Hammam-Rich maʻi pale: hōʻikeʻano

Hamman Rich maʻi pale - he kŘpa a ke nānā maʻi (mea hiki wale mai i umi wale hihia no haneri tausani kanaka), i hoike mai ai ia ia iho i loko o ka palapala o ka sclerosis o na maʻiʻaʻai a me ke kahua o ka ÷ naehana hanu ole. Poe akamai i ke kaila kona hanana i autoimmune keʻano o ka hanaʻana.

ka wehewehena

Hamman Rich maʻi pale - i ka maʻi pili i ka pathological kaʻina hana i loko o ka akemāmā'aʻaʻa, i hiki aku ai i kona sclerosis a me ka hooulu ana o naehana hanu ole. E hoʻopaʻa haʻawina ka mea, hoomaka ae la wale nō i loko o ka muliwai, o ka hope ke kenekulia, i ka wa a ka 'epekema nā puke pinepine paʻi puke a me nā wehewehena o like symptoms.

Kēia pathology mea oi, he pono ole i waena-elemakule a me ka poʻeʻelemākule kanaka. Ua Ua manaoio aku i keia i e ku pono i ka inoʻano, he hou loa o ka hana, a me nā 'ano o kaʻoihana kahuna, ai uala pono hana kūlana (welders, miners, e uhau ana, a no laila, ma luna o. D.).

synonyms

A kauka nana i ka mea mua, e noiʻi i ka pathology ua Scadding. He'ōlelo i ke kau e like me "fibrosing alveolitis." Akā loa koke ia i hoomaka ai e e ia i loko o kekahi, aole i palahalaha pono, denoting i ka pae o ka maʻi i i like symptoms. Nolaila, ka mea i oi ma mua o kekahi mau 'inoa.

Pathology Ua Kapa hou i ke Scadding maʻi, a laila, i ka Hamman Rich maʻi pale, e like me ka mea huli mai i ho'ākāka 'ia i kēia mau kauka mau like pathology i ka makahiki 1935 mamuli. Aia i nā synonyms o keia nosological pa alima, no kekahi laʻana, e holumua ai interstitial pulmonary fibrosis, fibrous dysplasia, cirrhosis, akemāmā purulent interstitial pneumonia a me na mea e ae. Ma ke kālā no lapaau, ua mana e hana mai ia lakou a pau.

etiology

Hamman Rich maʻi pale no koe kekahi o ka maʻi o ka ike ole etiology, mai ka kŰia o ka fibrosis 'ia i loko o kēia maʻi o ke akemāmā'aʻaʻa nonspecific naoh i ka pathological kaʻina. Ka loa hanohano i loko o ka 'epekema kaiāulu i ka pähola' ana i ka maʻi ua kena ae la ia e ka autoimmune kaʻina hana ma muli o allergic reactions o ke kolu o ka 'ano (immunocomplex).

Aia mau proponents a me polyetiology kumumanaʻo. Ka mea hoʻopaʻapaʻa i ka akemāmā'aʻaʻa ua paku ole ia i kekahi mau konohiki o mea koʻohune, fungal a mea hoʻomaʻi ano, i hiki aku ai i hyperergic naoh o ka'ōnaehana paleʻea nenoaiu.

No ka helu o nā kānakaʻepekema noonoo mua-Rich maʻi pale Hamm me kekahiʻano o ka collagenosis, kahi o ka pathologic kaʻina mea i kaupalena 'ia wale nō ka malamalama.

pathogenesis

Huʻi interstitial pneumonitis (Hamman Rich maʻi pale) akaka aie i ke kahua o ka ai-kapa alveolar-capillary pa alima. Mai pehea kāheaʻia pathological loli hilinaʻi nui ma luna o ka maholahune uku o kinoea i loko o ke koko, a, me ka a no o ke hypoxia. Kēia kaʻina mea i kū hoʻokahi a hiki i keia kekahi maʻi, a me ka typical naehana nā loko pane i ka hewa.

Hoemi i ka maholahune o kinoea ma na alveoli ia lŘlŘ no kekahi mau kumu. Mua, i ka loli ana o kaʻili lahilahi kona mānoanoa, a i pohā like fibrinogen mea i loko o ka wai koko, permeates kēia mau mea, e ia oi anuanu a me kaʻoʻoleʻa. Ka lua, ka epithelium naʻau i ka airway sacs (alveoli) maloko i cubic, a haalele i kona waiwai. Apana, e nee perfusion kaʻina kinoea, oa ka makani e komo ai ka ia maʻiʻaʻai,ʻaʻole ma ka hui 'ana me ka circulatory'ōnaehana o kekahi keia kaʻina ia lŘlŘ nui koke. Eia hou, aia no he reflex spasm o na moku o na maʻiʻaʻai aie i ka mea i loaʻa i loko o ka puʻuwai o ka pulmonary holo, a hoi exacerbates ka pathophysiological maomeka.

symptomatology

Hamman Rich maʻi pale i loko o nā keiki mea pohihihi keia. Kēia maʻi ka hapanui ia lŘlŘ ma waena-elemakule a me ka poʻeʻelemākule, akā, i ia ma premature keiki me ka hoemi uku 'nona iho.

Ke kali hoouka kaua ana o ka maʻi. Ma kānaka, he mau Episode o maloo cough a me ka manao pono i loko o ka pahu. A laila, ka mea, ua hui ma ka pokole o ka hanu, a Exhale he hōʻemi iki ala ma ka wela, nawaliwali, luhi. Ma ka loiloi mua ninaninau pono i nanaia bluish fingertips a me nasolabial triangle. Malia paha he loli o ka maʻi phalanges, a kui shape.

Aia hōʻeleu i Kal, uuku ua pohā rales i loko o ka ia maʻiʻaʻai. Me ka maʻi Holomua pinepine Episode o ka puʻu, sputum akaka, a me ka pohihihi keia hihia a me ka hemoptysis (ka wā i loaʻa capillary nahā i).

lapaʻau '

Eiei? Interstitial pulmonary fibrosis (Hamman Rich maʻi pale) hiki ke 'akomi i na mea o ke keʻena hoʻokolohua ho'āʻo wale nō i loko o ka maʻi kahua o ka hoʻonaʻauao, e like me ia ma ke koko ho'āʻo nō e' ole-kekahi loli:

• e māhuahua kumuʻiʻo;
• SSCHE hoʻonui (erythrocyte sedimentation kōmi);
• loli ma ka lākiō o ke kumuʻiʻo hapa.

Mau huahelu hōʻike i ke alo o ka li nui, akā, i ole e hōʻike i kekahi o kona ano, aole hoi ma o ka wahi. A kona wahi ke kōkua kumumanao radiography o na ia maʻiʻaʻai. Ma ka loiloi mua kahua o ka hoʻonaʻauao he mea he lālā hua kumu i loko o akemāmā aa, alaila, he upena graininess akemāmā'aʻaʻa. Over manawa, na paʻi hōʻike wahi o ka mahuahua mäliko, a lawe i ke kino o ka waihona meli. Heart E e hoʻololi i aie ai i ka hua o ka naau pololei.

palena pauʻike,

Hammam-Rich maʻi - he maʻi i mea ole, e diagnose kaʻoi loa, no ka nonspecific loli ma ka ia maʻiʻaʻai. I mea e pololei eʻoiaʻiʻo o kaʻike,, e hookaawale ia na mea a pau e ae.

Ke kauka pono e e like me kā:

• ʻawahia a allergic alveolitis fibroziruschim;
• ʻeluaʻaoʻao pneumonia;
• sarcoidosis;
• hoʻolaha pulmonary tuberculosis;
• systemic connective'aʻaʻa maʻi (lupus, rheumatoid arthritis, scleroderma, etc.);
• akemāmā Ka maʻi 'aʻai;
• pulmonary hemosiderosis;
• pae o ka pneumoconiosis.

Wale nō i loko o ka hanana ana a pau o na koho luna i kāpaeʻia diagnosed maʻi pale Hammer-Rich. pono e lawe mai postmortem ninaninau pinepine. E hana i kēia, i ke kauka prescribes ka hamama a paʻa kui kele ma biopsy, ke kaumaha ma muli o nā kuʻina manao ia o ka maʻi.

morbid'anatomia

Symptoms a me kaʻike, Hammam-Rich maʻi pale hilinaʻi ma luna ana o nā loli ao holoʻokoʻa ma o ka akemāmā'aʻaʻa. I mea e loiloi i ia, wehe i kekahi'āpana o ke akemāmā, a huli aku ia ma lalo o ka microscope. Nā hopena o keia ao i ole coincide me ka lapaʻau hoikeana, akā, ka mea, ua oi pololei, no ka mea, noonoo 'ana i ka moku'āina kino.

Inā ka maʻi mea ma lalo o fibrosing alveolitis, ka pathologist ike'aʻaʻa haanou ana wai a me ka maʻiʻo kiʻekiʻe o fibrin i loko o ka alveolar lumen, impregnation i pohā hoʻoʻino pane keena. Inā ka pathological kaʻina progresses, ia mea histologically akaka no loli ma ka halepaahao me nā hale a me ka endothelial alveolar capillary hale ilaloʻili lahilahi hanaʻia naʻe. No hoi e hiki hapa ka make ana o na alveoli i loko o ka wahi o ka hui 'ana me nā ipu.

Aia he elima degere o ka loli i ka ia maʻiʻaʻai.

1. Edema a me ke kelepona hele infiltration o alveolar pā.
2. Loli hoʻopiha i nā alveoli a desquamated keena a omo o ka exudate i pohā a me kona sila.
3. I ka make ana o na alveoli, ke kahua o cysts i loko o ka uuku bronchi.
4. Mau meakino a me ka uuku cysts.
5. "Kelepona hele" i ka malamalama no i nui cysts.

Course a me ka prognosis

Kelloidoz (Hamman Rich maʻi pale) i kekahi 'ano hune prognosis, no ka mea, mea hiki ole, e hooki aku i ka Holomua o ka maʻi. E like me ka lapaʻauʻia pathological kaʻina hiki e lohi, akā, ma neia hope aku i ka maʻi, e lanakila no. Ka hoomanawanui i ia mai i kekahi mau mahina i kekahi mau makahiki o ke ola. E like me ka makemake exacerbation a me ke kala ana i manawa lolelua ka iloko o keia manawa.

Over manawa, ka mea e holumua ai cardiopulmonary insufficiency hiki aku ai kanaka i kīnā o ke kino, a laila, e make ma ka asphyxia. I ka mea momona a hihia, ke hoʻomanawanui, e ia i kekahi, mai ka manawa o kaʻike, elima i ehiku makahiki. Eia nae, i ka mea, e hoʻokō i nā koi o ka kauka. Ma pohihihi keia hihia, i ka hopena hiki ma hope o kekahi mau mahina, nānā 'ole o ka Inc. Inā ka iapaau ana ua hoʻopaʻa 'ia no nā kuʻina kakahiaka nui o ka maʻi, i ka pohihihi keia manawa ia mea hiki i ka "malama" ia ma keia kahua a me ke kanaka ka ola, a me ka hoahanau ola hoola.

lapaʻau

He aha e hana mai, ma hope iho o kona diagnosed me ka maʻi pale Hammam-Rich? Lapaau hoʻomaka koke. Ia mea,ʻaʻole e pono e hoʻokaʻulua i ka hoʻomaka 'ana o ka lapaau, e like me ka maʻi progresses ma luna o ka makahiki hou, a nui. I Kekahi Mau lapaʻau ua ole i ke kino, no laila, kauka ho'āʻo e hooki aku i ka symptoms, a 'ūlōlohi mai ana i ka mämä holo o ka'aʻaʻa fibrosis.

Ma nā kuʻina ka loiloi mua o ka maʻi i ka loa ka hoʻokō ai steroid. Ka mea, emi ka hoʻoʻino hoikeana: exudation o ka loli, ke kelepona hele infiltration, 'ūlōlohi mai ana i ke kahua o connective'aʻaʻa, a me ka? Iecaianoaaiiie o nā mea'aʻaʻa. Bolus Inc hana, a laila hoʻomaka me kiʻekiʻe nā māhele (mai ka 60-80 mg no ka lā) a me ke kiʻekiʻe o emi i ka nui o ka lāʻau i ka 20 mg. He nui ke kanaka hoʻoponopono i ka ha awina o ka adrenal cortex, no laila, i ole e i Kushingoid maʻi pale.

Ma ka hope kahua o ka hoʻonaʻauao, ka wā lawa haʻi fibrosis, ua haawiia mai i ka ai 'i inhibits ka'ōnaehana paleʻea kahua koho. Special haawi aku ana i ka hoʻohui pū Inc o steroid a me cytotoxic ai '. Ka mea, ua oi mana ma mua o ka hoʻohana ana i kēia mau ai 'pākahi.

Ka hoonoho like symptomatic Inc decongestants, inhalation o ka o oxygen ma lalo o ka puʻuwai, ke B nā wikamina, e like me antibiotics hoʻohana i mea e pono ai (ka wā ka hoʻopili i ka haumāna maʻiʻaʻai), cardiac glycosides a me diuretics (me ka hoomahuahua i loko o ka naʻau ole).