Ola kinoMaʻi a me nā kūlana

Symptoms a me ka lapaʻau o Landau-Kleffner maʻi pale

Landau-Kleffner maʻi pale - Ua loaa epileptic aphasia i loko o nā keiki. Ua Ua wehewehe aku 'aʻe' o ka olelo kuleana pili i. Ma keia hihia, e ae mai oe i ka articulating eiiiiiaiou o ka olelo (kani hooponopono hou ma ke kumu o na niho, olelo, a me ka puʻu), a me ka hiki, e kiko'ī a i ka phoneme i loko o ka Central ko mākou hopohopo'ōnaehana pae. Ma ke alanui, ia mea i loko o kekahi mau wahi i loko o ka cerebral cortex.

I ka maʻi i loko o ia lŘlŘ loa ola na keiki. Mua ka mea nele i ka hiki i ke hakuloli i ka mawaho a puni, a laila, hiki ole e expressive, pono a me kekahi hoʻonohonoho ka hoike i ko lakou manao. Ka mea i loko o ka lolo o ke keiki e pathological loli, hōʻike i ka EEG. Ka maʻi pale i ho'ākāka 'ia ma 1957 ma nā kānakaʻepekema - Landau Kleffner. No laila, i ko lakou mau inoa, a kapa aku i kēia maʻi.

Nā kumu o ka maʻi

Kumu o Landau-Kleffner maʻi pale uaʻaʻole maopopo hoakaka. 'Oiai, ma kekahi hihia, kauka ke hōʻike i ka ololi i alakai aku ai i ke kūpono' ana o ka maʻi. Ma ka wahi mua - o ka paʻa poo poino, loloʻeho, he parasitic maʻi, kena ae la ia e ka larvae o ka puaa tapeworm - neurocysticercosis. Ke kumu o ke e, a me ka autoimmune demyelinating maʻi, ma a he mea ka make ana o ke keʻokeʻo mea o ka'emi'ōnaehana - myelin. Kāhea i ka hooulu ana o ka maʻi pale i i hiki o ka li nui i loko o ka ipu paia i loko o ka'āina o ka lolo. Mau Kupuna i kaʻatikala o ka maʻi i ua pili me ka deficiency o mitochondrial naehana eiiieaena. I kekahi manawa, ai ka mea emi loa ka lahilahi cortex, kūpono ai i loko o ke keiki ulu i ka loli hemisphere.

Ka maʻi pale hiki e fulminant palapala. I ka mea i nehinei he mau-makahiki hoʻi i hāʻawe hele, e kamailio pu, a ua pono olakino keiki, a me ka manawa āna i kāhea mai, hiki ole e hoopaa, a me kekahi mau hua'ōlelo. I kekahi manawa, i ka maʻi progresses lohi, hunahuna i nā haalele i kona hiki i ka waha 'ka mākau hoʻokaʻaʻike, a kūpono pokole o aku o ka lanakila.

He aha e na symptoms?

wahine nä känaka 'epekema maʻi i ho'ākāka' ia ma ka au mamuli Alexandrov N. Sh Landau-Kleffner maʻi pale, ia olelo, he mea no hoi no ka mea, o ka mea no laila,-kapaia lolo plasticity. Ua ua like ina "restructured" e aho hana i ko lakou mau oihana. Ma ke kaʻina hana o kēia hou 'a me ka hoʻomōhala ana i ka? Aiaiiuie aphasia. Like o ka hihia a me ka loaa palapala, nā palapū a me ka mai, kena ae la ia ma kēia 'ano o ka pathology hiki ke diagnosed hoʻohana' EEG. Eia hou, i ka "mua bele" e lilo epileptic kāʻili 'ana, iʻikeʻia ma ke kao. Ka mea, i loko o 70% o na pu ma ka hoouka kaua o ka maʻi.

Puni i ka hapaha o na hihia a pau, i ka hoʻomanawanui haalele i ka olelo hana no ka mahina. Akā, ka hapanui o kona make ana ia lŘlŘʻaneʻane instantaneously. I kekahi manawa, he kamaiki hikiʻaʻole ia e haʻi i ke kani. Ka hapalua o ka hoʻomanawanui iki mai ike 'ano' kāna hana. Hana ana manaʻo ua malamaia. Me ka elemakule, ke kāʻili 'ana nalo. Full a hapa loaa o ka olelo hana ana no 16 makahiki.

mea hōʻemi o ka olelo

Landau-Kleffner maʻi pale i loko o ke keiki hoʻomaka me ka lilo ana o ka hana o ka olelo - keia mea kekahi o na kumu nui symptoms o ka maʻi. Ua Ua wehewehe aku ma ka waha a auditory agnosia - hihia hoʻi pokole, a malama i ka ike a me ka pā lonoaʻili. Ma ka hihia mua, i ke ahonui mea e hiki ke olelo pono. Ma ka lua o - ia i hiki ole hoʻomaopopo ninau i na ino a me nā mea kani-. Ma keia hihia, e maʻamau pane i PalekanaEND_LINK phonological audiogram.

I ka papa kuhikuhiE pilikia nō kaʻoi loa i loko o ka mahinaʻai o ke kani pā lonoaʻili. I loko nō o kēia, i ka maʻi pale hoike mai ai ia ia iho i loko o ka pilikia wā o ka 'ōlelo āpana noonoo. Hihia hoʻi olelo hōʻike hou hiki e pae okoa o ka manaʻo pohihihi. Aphasia mea nui ikaika i loko o kekahi mau hoʻomanawanui iki mai. E like me kānakaʻepekema i aku nei au, e diagnosed huikau hihia i loko o 6 hoʻomanawanui iki mai mai o 77. Inā ke keiki ua malama nīnūnē aʻe 'ana, ka mea hiki ke hoola i ka heluhelu a me ke kākau mākau. Language haunaele hoike like penei: ke keiki confuses palapala, a kani hewa e kūkulu pohihihi,ʻaʻole hiki kekahi hoʻonohonoho ka hoike i ko lakou manao, a no laila, ma luna o.

epilepsy

Lapaʻau ke kāʻili 'ana i mālama i loko o 70-85% o ka hihia o ka lilo ana Landau-Kleffner maʻi pale. Maʻi i loko o ka hapakolu o nā keiki i hoʻomaka me ka hookahi epileptic 'ana. Keia mea - o ka hoʻomaka 'ana o ka maʻi. A helu o nā mea maʻi ma waena o ke kaua a me ka olelo kāna hana i lawe kekahi mau makahiki. Kāʻili 'ana i pinepine paa ma ka makahiki mai ka 4 a hiki i 10 makahiki. He nui nā kauka e olelo aku i ka mea e ole i ke ana i loko o kanaka makua ke ola. Ia mea, ma hope o 16 makahiki o ke kāʻili 'ana mai i kānāwai.

I ka 58% o nā mea maʻi me ka haka pono ka helehelena ke kāʻili 'ana. Kā lākou mau mea, lalau mai hoʻopilikia maoli i ka lolo aeee i loko o kekahi mau 'āpana o kekahi cerebral hemisphere. Ke kāʻili 'ana ma ka 39% o nā keiki, hopu me ka poho o ka ike paka i - i 16%. Kekahi e hoomanawanui i hooleiiaʻi mawaho myoclonic kāna hana mea e pono ai na nāʻiʻo o ka maka, a me ka maka na ohia. I ka 12% o nā mea maʻi epilepsy ua pū i hiki i ka aaiaoe kiʻekiʻe.

'ano' kāna hana

Ka mea, ua ano no ka aneane pau loa nā mea maʻi. 78% o nā keiki opiopio i 'ano' pilikia ina ka mea, i diagnosed me Landau-Kleffner maʻi pale. Nā mākua e ole e hopohopo ia e ka mea i kā lākou koke maluhia a me ka pili aloha kamaiki koke liloʻano pākīkē. Huhu - he maʻamau symptom. Huhu hiki e ai, pili a me ka uncontrollable, i ke keiki hiki ole ke hoʻolimalima hale e Makuakane me ia me hospitalization i loko o ka psychiatric kula. Others, ma ka mea ku ole, e hoihoi ho opa ao. Ka mea, pale aku i ka poe o ke kanaka e loaa ana mai ka iini a me ka obsessive manao.

he keiki kekahi e e loa kuli. Kekahi poe e ae i ka mea hewaʻike, - autism. Aia hoʻi, kauka i kekahi manawa, paʻakikī, e hooholo i ka maoli kumu o ka'ē hana o ka Landau-Kleffner maʻi pale. Ma hope o nā mea a pau,ʻo ia a me autistic hana wehewehe aku ma kaʻike manaʻo e like me ka hikiʻole, e? Ieoaeunoai Logical completeness o ka manaʻo, ka obsessive repetition o ka ia nä hopuna, olelo. Nawaliwali lehulehu o ka noonoo ana, a mahuahua aayoaeuiinoe malama i ka 80% o nā mea maʻi. ʻOiai 'ano pilikia e kiʻekiʻe symptoms ma ka pili olelo pilikia ia, na keiki kekahi i kähähä hana, illogical a me ka bizarre reactions. No ka laʻana, ka mea hiki ke pana aku au i nā hola hou i ka hookahi lima kolohe 'ana.

kēia Inc

Ma ka hoailona mua o ka maʻi, he pono e hoʻomaka lapaʻau o Landau-Kleffner maʻi pale. Ke? Aaieou, i loko o ka mea au i kapa, e e hiki, e kaumaha aku i kekahi pāʻoihana i ka pilikia.

  • Lāʻau papa;
  • ʻoki kino.

Ma ka hope Ina, i ka hoʻomanawanui wehe i ka puniu wale no, a wehe epileptic pulakaumaka. E hana i kēia, oki ae la kekahi o na iwi, a no ka paakiki iwi o ka lolo. Ma hope o ia, i ke oho mea o ka surgeon i ka incision. Ka mea, e hoʻomau i ka pale aku i ka outbreak a me ka laha ana o epileptogenic lāʻau ikiʻai wale. A laila, i ka dura mater, a me nā iwi i waiho mai ai iloko wahi. Kaʻeha ua sutured. Mahope o 6-7 pule ma hope oʻoki kino, ke keiki, mai ka haukapila hiki hoʻi i ka hale. Ma hope oʻoki kino i na keiki me Landau-Kleffner maʻi pale ike hou ana i ka 'imi naʻauao a me ka manaʻoʻike i hana'.

Anati-kāʻili 'ana i

Lapaʻau o Landau-Kleffner maʻi pale mea,ʻaʻole mau hoakaka wale hana ana Lolina. I kekahi manawa e kōkua i ka pakele ana i ka maʻi 'inikua Inc. Ua hāʻawi? Eaia o anticonvulsants. Eia naʻe, ka mea e ole e haawi mau i ka maikaʻi result. No ka laʻana, "carbamazepine", "Phenobarbital", "Phenytoin" i pinepine ineffective - aphasia hiki wale kiʻi ino. Hopu i loko o nā mea maʻi e e hai hou me ka hoʻopaʻiʻana. He oi loa oiaio o nā mea maʻi me ka pinepine kāʻili 'ana a me atypical kaawale ke kāʻili' ana.

Eia hou kekahi, kauka pinepine waiho aku "Nicardipine". Ua kōkua e aeie kalipuna kaha. Mea pono keia mau mea i ka hooponopono ana o intravenous gamma globulin. a me ka mea i hooiaio pono ka hoʻokō lāʻau "ethosuximide," "valproicʻakika". Help a me benzodiazepines, o ka oi aku "Clobazam" a me ka "Midazolam". Akā, ka mea pono e lawelawe intravenously.

'ē aʻe ai'

Landau-Kleffner maʻi pale, symptoms a me ka ohe. A i ho'ākāka 'ia i loko o keia' atikala eaaaony no ka hiki aku o "Diazepam" mua ka hele ana i kahi moe. Kēia lāʻau haawi maikai hopena. Inc ua hoakaka ia no ka manawa o 6 pule, e pale aku tachyphylaxis - kokololio ka ho'ēmiʻana kanawai me ka hai lawe ana i ka waiʻona. Haʻawina i hōʻike i ka mea i pono keia mau mea e "levetiracetam". Ua Ua hoi loa pono kōkua ma ka iapaau ana o ka noho 'ana kamaliʻi idiopathic mea nui ke kāʻili' ana, epileptic uila kūlana o ka hiamoe, suppression o ana SPIKE hawewe i loko o kona lohi pae. Eia hou kekahi, holomua ma ka lapaau ana o aphasia a me ke kāʻili 'ana, me ka lāʻau "felbamate." Akā, i ka wā e hana ia mea hiki ke kūkulu i kekahiʻano o kaʻaoʻao waiwai, i waena a me ka loa pinepine pilikia aplastic anaemia , a ake dysfunction.

corticosteroids

Ma ka iapaau ana o Landau-Kleffner maʻi pale a me ke kōkua corticosteroids. "ACTH" pakahi aku la ia pono-ai. Ua ho'ēmi i kā ka hoike ana mai o symptoms o loaa epileptic aphasia, normalizes ka moku'āina o ka EEG. Lōʻihi-ʻia Inc me kēia mau ai 'ua pono loa o ka hoʻomanawanui iki mai. Eia naʻe, e makaala i ole a pau ka pono hormonal kanaka koho.

Pinepine kauka i hoakaka ia steroid i nā mea maʻi. No ka laʻana, "Prednisolone" ua lawelawe intravenously maluna o na malama ekolu. Ke Inc ua hoʻohana no ka mea e kalaiaʻi hoʻokomo. He nui ke lawe i ka manaʻo i ka ka ho'ēmiʻana i loko o ka laʻau heluna o steroid i ua pinepine pili me ka ikaika recurrence o ka maʻi symptoms. Ka huina lōʻihi like 'ole o ka holo ana hiki mau mai na malama eono a hiki i kekahi mau makahiki. Incidentally, corticosteroid lapaʻau i ka hailonaʻana o kaʻaoʻao 'ole e like me ke kaupaonaʻana ka waiwai, hypertension, mimikō, cataracts, hakuʻala e hemahema, kaumaha, manic maʻi pale, a no laila, ma luna o. Eia hou kekahi, aole lakou i ole e waiho no e hoomanawanui i ka poe i pilikia i hoʻonele, e like me ka mea hou e kaumaha ana ia ia. Ka mea, i kekahi contraindicated i kanaka me ka aseptic necrosis, tuberculosis a maʻiʻo konaʻano hoʻonāukiuki aku i ka nui mana o roundworms.

I ka manao o na makua

Special malama a me ka noonoo ana ua koi no ke keiki diagnosed me Landau-Kleffner maʻi pale. Reviews o na makua hōʻike 'ana i ke kamaiki pono e lawe papa i ka olelo kino, olelo pathologists. Ke kauka hiki ole e hoihoi olelo kuleana pili i. Akā, i kēia mau kau ao na hunahuna i ka perseverance, e lawe mai i loko ona kuleana, hui. Makua hoʻopaʻapaʻa ana i kamaliʻi ma waho no laila, i koi 'ia i ka anticonvulsant maikai a me ka antiepileptic lāʻau i kapaia "Keppra". Mākou i paipai aku "Depakine," akā, ia pinepine i ka hopena maikaʻi 'ole ma o ka pancreas, no laila kekahi ka hoʻololiʻana i ka homeopathic lapaau. He nui makuwahine a me nā mākua, ua kaulana no hoi i ka mea momona a ala me ka maʻi pale -ʻoihana kaua, pēpē. He loaʻa kaikuaʻana - ua ke kiʻekiʻe o ka hoʻomaikaʻi i ka olelo ana. Eia hou kekahi, makahiki-holo ho'āhewa wale a me paroxysms.

Outlook

Like no na kumu, ka mea hoi e hoʻomau e makaikai i mea i Landau-Kleffner maʻi pale. Photo hoʻomanawanuiʻana a me kā lākou mau wikiō Episode, mōʻaukala, manao hoʻomalu ololi holoʻokoʻa - a pau i kēia mea hapa o ka noiʻi. Kauka i kekahi 'i ka Inc hana maikaʻi i loko o ka hanana i ke keiki mālama nei psychotherapy, olelo papa. Full loaa o ka 'ae waha' oihana, he 'ano pohihihi. IeAUPIIe, IAa IO 2/3 o nā keiki i ho'ōla oi a emi mea olelo uuu no.

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