U ka pentad: mea, lalau mai, lapaʻau, prognosis

Aia ka he wahi lihi iki o ka malformations i hanaʻia i loko o utero. Ka mea, e loli i kekahi hui, nenoaiu. Ka noho pilikia loa i ka naau mā, akemāmā, digestive nenoaiu, puupaa, a me ka lolo. i incompatible me ke ola kekahi o ia mau mea. Other amenable iʻoki lāʻau lapaʻau lapaau. Kekahi o ka loa luna 'malformations noʻonoʻo pentalogy U. Kēia maʻi ua wehewehe aku ma ka helu o nā 'aʻe' ana o kekahi mau nā loko. Ma kekahi mau hihia, e hiki ke loaʻa i kāpili pentad U. I loko nō o ka oolea o ke kina, i kekahi manawa, i hiki ke Makuakane i ka maʻi, a hoihoi aku i ka nui mana o ke kino kauka.

U ka pentad - He aha ka keia pathology?

Kēia pathology ua pili i ka congenital naʻau maʻi, a me nā nā loko. E like me ka inoa pentad U nā 5 mā. Iwaena o lakou o ka noho pilikia loa kue ana i ka mea'ōnaehana mānowai koko oihana, a entails i ka loli ma ka hemodynamics. I keia kina komo ai weliweli mea hoʻonani kina. Ike ka mea, hiki e koke i hanau i ke keiki, e like me ka naau o ke keiki "na newa mai". U ka maʻi pale, aole ia e mau loa ana me he poe 5 mā. Pinepine i 1 a me 2 kāna hana ma kahi e (tetrad triad). Ma waho aʻeo ka naau mai, i ka maʻi kikowaena kekahi kaumaha symptom - omphalocele. No hoi he mau loli i loko o ka anterior abdominal a me ka umauma pa, diaphragm kina.

U ka pentad: ke kumu o ka maʻi

He nui ka ike i ka maʻi ua hanaʻia i loko o ka lua o ka trimester o ka hāpai keiki. I loko o kēia wā, e waiho ana i ka nui nā loko, a nenoai. E like me ka mea, ua ike, no ka 14-18 pule o ka hāpai keiki i hana mesoderm. Ma lalo o ka aoao o ke? Aneie aʻe a me kela nā mea palahēhē makuwahine kekahi aʻe 'ana o ka embryogenesis e hana ana i kēia wā. I kekahi o kēia mau abnormalities hiki e pentalogy U. Ke mau kumu o ka maʻi i ole, ua hoʻokumu. Naʻe, i kēia kina ua pili me ka chromosomal abnormalities. I waena o lākou, 18 a me ka trisomy 13, Turner maʻi pale, X-ua hoʻopili maʻi. Ua ua ike ia keia kina mea he pohihihi keia. Ke alapine (frequency) o kona hanana mea 3-5 keiki no miliona. Ma ke ao nei o ka emi o 100 hihia i hoakakaia. Ka maʻi Ua oi, he pono ole i na keiki.

I loko nō o ka mea e, e loaʻa mai i ke kumu kumu o ka maʻi i ole hoi ia, e pono e ike e pili ana i ke kamepiula kumumea i alakai i ka likeʻole kāna hana o fetal? Acaeoey. I waena o lākou:

1. I ka hopena o nā palapala a me kaʻawahia waiwai (paʻakai o ka mea kaumaha i eliiaʻi, ai ', a me Nine Inch).
2. Ka pāhawewe ke waiū.
3. Helu ciia (eha).
4. Stressful wahi, i hiki.
5. Puhi paka a me kanakaʻona mau nā mea inu.

ʻano papa hana o hemodynamic kāna hana

Aie i ka mea i ka pentad U ke 'ike kekahi naau mā, hemodynamic haunaele, ke'ōlelo mai oko mai kekahi i kekahi. Loa pinepine keia maʻi ua pu ma ventricular septal kina. Ka hooulu ana o hemodynamic kāna hana hilinaʻi nui ma ka hope. Me ka nui mā ana i ka nui shunt liʻiliʻi kaiapili, ma ia e alakai i ka pulmonary hypertension. Ka hema ventricle ua overloaded a me ka uku 'hypertrophy. E like me ka hopena, he mea i ulu i loko o nā ka RV a me LV.

Emi, he pono ole atrial septal kina. Hemodynamic haunaele ia mea, ua hilinaʻi nui ma luna o ka nui o ke kina. Me ka 'ōlelo he nui ma waena o ka atria hookuuia ana o ke koko i loko o ka pono, hookaawale ua me ka nui loa, a mahuahua nui, kūpono ma ka hypertrophy a me dilatation o ka PP. Ka haʻalele atrial overload ia lŘlŘ.

I ka papa kuhikuhiE hoikeana o U ka pentad

E like me uaʻike, ka panina U maʻi pale nā 5 mā. Iwaena o lakou i na kēia aʻe ':

• Omphalocele fetus. Ma kekahi alanui ka mea, ua kapaʻia kekahi keena-umbilical abdominal pā kina. Kēia 'aʻe' Ua wehewehe aku ma ka mea i ka na nā loko maʻamau i loaʻa i loko o ka opu, e ohi i ka umbilical hernia eke, a hele aku iwaho.
• Umauma pa kina. Ua Ua loa olelo wehewehe aku ma ka wa e kaawale aku ai ka mahae xiphoid. E like me ka hopena, o ka naau ua kekahi neʻe mua.
• I ka wa e kaawale aku o ka pericardium, i mea e e pili ana i ka diaphragm.
• Cardiac anomalies ulu. Maʻaneʻane na hihia a pau i ka ectopia - pololei ole i hoʻokomo 'oihana i komo. Ma keia naau kina hiki ia ma ka abdominal paha'ā'ī. Eia hou ectopia, a ma laila e like mā. Ma waho aʻeo i ka VSD a me ASD ia lŘlŘ atresia o ka tricuspid kiwikā, i ka pulmonary artery. Ma pohihihi keia hihia, no ka piha kaawale o ka naau keʻena.
• Diaphragmatic hernia.

Ma waho aʻeo ia U maʻi pale i e kāpili, a me ka mea, ua ike no hoi me ka hoʻohui pū ana i nā anomalies. Loa pinepine, i kēia maʻi o ka CNS (lolo hernia, hydrocephalus), gastrointestinal (pathology o ka laau awaawa, a me ka bladder spleen), i ka wa e kaawale aku o ka manamana lima a me lala.

Ka lapaʻau kiʻi o ka maʻi

Nā symptoms o ka maʻi i maopopo mai ka manawa mai o ka hanau ana. Ka mea mua i ia iho, ike nui mea hoʻonani hewa i loko i ka naau a me ka abdominal nā loko "mahaka mai" waho. Eia hou, ma ka hora mua o ke ola, a hui hou weliweli symptoms. No ka mea, o ka congenital naʻau mā keiki loaʻa iki ka oxygen. E like me ka hopena, oia, he pokole o ka hanu, cyanosis, indrawing o intercostal hakahaka, a me ka haʻahaʻa o ka sternum. Loa pinepine, pono e pili ana i kēia mau keiki i ka ventilator. E manao i ka maʻi, he mea pono e loaʻa mai ma ka naau, e hoopaa i kekahi o na kumu nui hiʻona - ectopia kino.

He aha ka i kaʻike, a U ka pentad?

U ka maʻi paleʻike, ua ma muli kuhikuhi ma ka mawaho ninaninau ana o ke keiki. Mua, ke kauka nana no i ke alo o ka omphalocele - he kina o ka abdominal a me ka thoracic pā, a laila e hoʻoholo i kahi o ka naau o. Ma ka hōʻoiaʻiʻo aku o ectopic, kāna hana o naehana hanu a me ka hemodynamic kiko'î, i kaʻike, ua kokoke kekahi. E kau i ke alo o ka naau mā, hana auscultation a me ka echocardioscopy. Ultrasound o ka abdomen hana impractical no ka mea mua o nā mea a pau mā pono e eliminated.

Iapaau ana pentad U

I loko nō o ka mea i ka pentad U - kēia ua hui a me ka weliweli Hope, ma kekahi hihia ia mea hiki ke Makuakane me ia. Ua pili i nā mea maʻi me ka hemodynamic abnormalities hana maʻalahi me ke ola. I ka papa kuhikuhiE kina lapaʻau - heʻoki lāʻau lapaʻau 'uao. Ke hana ninoieo o kekahi mau kahua o ka hoʻonaʻauao, a ua manaoia kekahi o ka toughest. Ke incision ua hana i loko o ka midline thoracic a me abdominal pa. I ka Ia manawa, surgeons e lawe mai i ka? Iaea o ka naau mā a me ka ho'ēmiʻana o ka digestive nenoaiu. Ectopia o ka naau ke ana i koe. Ma kekahi mau hihia,ʻoki kino no ka poe liilii, a me VSD ASD moe ana i ka nui kupono makahiki (3 makahiki).

Kāohi malformation

O ka papa kuhikuhi hana o ka Kāohi mea i prenatalʻike. Ana diagnosed pentalogy U ma ka fetus hiki ke haawi mua ma 20-24 hebedoma o? Acaeoey. Loa pinepine, e like me ka hopena o ke kumu no ka hoopau ana i hāpai keiki. No ka iniiaiie Kāohi nā:

• E pale nā palapala 'ole.
• Malama i ke ola i ke Aloha Hawaii.
• Pale stressful wahi, i hiki, o ka oi aku i loko o ka hapa mua o ka hāpai keiki.

Ke prognosis o keia maʻi i kekahi henua, e like me ka mea hilinaʻi nui ma luna o ka degere o ka poho i ka naau. Ma kekahi mau hihia, kauka kahu ai e hoola i kekahi keiki ka ola. Aka hoi, i kēia mau keiki pono mau malama a me ka hooponopono ana o hoʻomalu.