Ola kino, Maʻi a me nā kūlana
Ke anomaly o Arnold Chiari
Anomaly Arnold Chiari pu aku dystopia ( 'aʻe' paʻamau) nā hale i loko o ka posterior cranial fossa offset ia ma o ka nui hanau'ā'ī mawaho o ka puniu wale no i loko o ka spinal Canal. A naeaeaa cerebellar tonsils a hapa i ka luna o ka vertebral Canal.
Aia mau eha ke ano o keia maʻi. Anomaly Arnold Chiari Type 1 ua hōʻike offset cerebellar tonsils,ʻaʻole pu ma nā anomalies lolo ulu. Kēiaʻano ike i loko o kanaka ma hope o kanakolu makahiki. I ka lua o kaʻano o ka 'aʻe' ana i na wahi o na hale a ma ka posterior fossa a me cerebellar tonsils. Loa pinepine i kēiaʻano ua diagnosed i loko o nā keiki. A koluʻano o ka anomaly mau wahi nā 'aʻe' ana o aneane pau nā hale ma zadnecherepnoy fossa. I ka hoike ana o keiaʻano mea i hana maʻalahi me ke ola. I ka ha o kaʻano o ka anomaly ua inherently manaoia he oko o ka underdevelopment o ka cerebellum. Hoikehonua, neurosurgery pili ia i Dandy-Walker maʻi pale.
Ma cerebellum indentation i loko o ka hapa luna o ka spinal Canal mea he hana maʻamau o ke outflow lama ia i malama i ka lolo a me ka spinal kaula. Abnormalities ma CSF holo hiki i blockage o ho'īli lepa mai o ka lolo a hiki i na nā loko a hoʻomāhuahua o cerebrospinal loli. Ka puʻe i ke cerebellum i ma ka spinalʻula i ka hopena i syringomyelia.
E like me ia he nui akamai, Arnold Chiari anomaly ua manaoia e e he hereditary maʻi. Naʻe, ka mea e e hoʻomaopopo i nā haʻawina pahuna ma investigating keia ololi, eia ma ka loiloi mua ke kahua.
He nui nā mea maʻi e loaa ana mai o keia kāna hana, ka mea, ua i malama i na hoailona a me symptoms. Ia e hoomanawanui i loaa ole lapaau. Ka loaʻaʻana o ka maʻi ia lŘlŘ wale nō i loko o kaʻike, o'ē aʻe ka maʻi.
Ka hooulu ana o ka maʻi i loko o ka hapanui o na pu ma ka headache, hoonaukiuki ma ka puʻu, kiheʻana a physical overexertion, numbness a tingling i loko o ka lima, ma ka 'aʻe o ke ana wela-ikepili koʻikoʻi, a me ka hopena, pinepine'ā. Eia kekahi, no ka mea, he maʻi wehewehe aku ma kaʻeha ma ka cervical a cervical māhele 'āina, a hiki i kekahi manawa ihona hene mau poohiwi. Aia nā pilikia i ka malama ana kaulike (haoʻa gait) a me ka hoʻonāwaliwali maoli nō i ka ōhumu lima o.
No ka mea, he nui no na symptoms o ka maʻi ua pinepine pili i nā illnesses, ia mea e pono ke loaa i ka pihaʻike.
PalekanaEND_LINK ana hoʻomaka me ka hookolokolo a me ka hoʻomanawanui ninaninau. Inā ka hoʻomanawanui complains o kaʻeha i loko o ke poʻo, akā, i ke kumu no kā lākou hanana mea i ike i ke akamai kanaka, ka mea e e häʻawi mai ai iä MRI. Lapaʻau 'apono' lawa pololei e hōʻike ana i ke alo o ka maʻi.
Ma kekahi mau hihia, Arnold Chiari anomaly i kekahi e holumua ai maʻi e hiki aku ai i ka mea nui complications. Mau nā hydrocephalus (oi loli i loko o ka lolo). Pela ka mea, ua pono no i'ōlewa Tube no pumping ka cerebrospinal loli a hiki i kekahi wahi o ke kino. Complications o ka maʻi i nā lōlō. Ua hoʻomōhala ana i like me ka hopena o spinal mīkini'opihia. Syringomyelia pili no hoi i hiki complications. Ua Ua pu ma ke kahua o cysts i loko o ka spine a me ka lua, a ua hoopihaia me ka cerebrospinal loli, a haawi aayoaeuiinoe.
E hoomanawanui i ka poe i ka Arnold-Chiari abnormality lapaʻau ua haawiia mai ia e like me ka oolea o keʻano. I ka hele ana o symptoms, ana i kauoha mai ai ma ka pololei, ka mālamaʻana a me ka nānā 'ana. A hiki i ka hoike ana mai o symptoms o iniiaiie kauka i hoakaka ia painkillers. Naʻe, ka hapanui o ka lapaau ana i ka maʻi ua hana surgically.
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