'O Badda-Chiari Syndrome

'O ka ma'i Badda-Chiari e loa'a mai i ka hō'emi'ana (pani'ia a'ōwili) paha o ka māmā o nā māmā e holo i loko o ke ake. Ua mana'o'o Chiari ke kumu nui -'o ia ke kumu nui o nā ma'i hepatic. Akā ma nā hihia i lalo, ua'ike'ia ka thrombosis o ka ma'i hepatic a me ka mea kino ha'aha'a ma kekahi mau'ano.

Ke moʻokalaleo wehewehe o ka hola 200 hihia o obliterating endoflebita ma hepatic aa koko (maʻi , Budd-Chiari maʻi pale).

Me ka ho'omohala'ana i nā ulia o ka aranzian, kahi e holo pololei i ka hepatic hema, a me ka vela umbilical, hiki ke ho'omohala kēia ma'i i ka wā'ōpiopio. Ka loko iwi o ka hepatic aa koko a emi iki mahope o vena Vienna (ma kahi o ka confluence o ke akepaʻa) ua e ulu ana, i kekahi manawa, hui ma ke koko clots. 'O kēia mau mea ka hopena a i'ole ka'ōiki o ka lumen o ka vein, a, ma ka hopena, ke kumu e ho'onui i ka loli a me ka ho'oikaika o nā pūwa'i.

Budd-Chiari maʻi pale e hoʻomōhala ana i kekahi i loko o ka 'ē aʻe pathologies: malignant neoplasms o ke akepaʻa, pancreas, hakuʻala, etc., vascular mai generalized ano. Hiki i ka pelrhosis o ke ake i ke kōkua i ka pa'akikī o nā ma'i hepatic. Hiki iā ia ke hana i ka ma'i ma'i Chiari me kekahi'ano localization o ka'āpana, echinococcosis, actinomycosis, abscesses a pēlā aku.

'O ka ma'i ma'amau,'o ka Buddha-Chiari ma'i e hō'ike iā ia iho he hō'ailona o ka ma'i ma muli o ka hopena, a'o ia ho'i, ke hilina'i nei nā hō'ike i ka lō'ihi o ke kau'ana o nā māmā. Ke hō'ike'ia nei ka ho'omaka'ana o ka ma'i a'oi aku ka iki a me ka mālie.

'O ka pa'i nui'ana o nā ma'i hepatic i ka hopena o ka lua'i'ana, ka'eha ma ka pono hypochondrium a epigastrium paha no ka ho'ouhu'ana o ke ake, a me ka poho o ka capsule'āpala, ascites e ulu ana, kahi'ike iki.

Komo Nā hypertension e hoʻomōhala ai i ka mea ia manawa, no ka mea o ka mea kokololio mahuahua ma ka puʻe i loko o ka hepatic sinusoids a me aa koko.

Hiki'ole ke mālama'ia ka ma'i i loko o kēia'ano ma'i,'o ka wai e wikiwiki koke'ia ma hope o ka paracentens, i kekahi manawa ka'ume'ana i ke koko i loko o ia mea,'o ia paha ka ulu'ana o ka hydrothorax. Inā hāpai ka thrombosis i ke kino li'ili'i, e ho'oulu i nā lālā lalo, "po'o kelekele", a me ka hopena iki'ana o ke koko, e pi'i i luna.

Me ka ho'oikaika'ana i ka uhi'ia'ana o nā māmā o ke ake, e pili pū'ia ka thrombosis o nā moku i'a, ka'eha a me ka ma'i'ana, nā pilikia o ke'ano neurological no ka hō'ino'ana i nā pūpa'a, a me ka hopena o ka make ma kekahi mau lā.

I kekahi manawa'o ka ma'i'o Badd-Chiari, me ka pani'ana i nā vein, hiki ke hana'ia e like me ka ma'i mau lō'ihi no ka wā lō'ihi. Me kēia'ano o ke kahe'ana, hiki i ka hanu holo'oko'a ma kahi o ka manawa: e pālahalaha nā'ili o waho o ka'ili,'ike'ia ka hanu o ka puka pā, a laila e komo i nā kolo varicose o ka esophagus.

No ka hana'ana i ka hō'ailona,'o ka hiki'ana o kahi kaomi i ho'okomo'ia i loko o nā māmā o ke ake a me ka ho'onui'ana o ka pihi puka e mea nui, e like me ia i hō'ike'ia e nā'ano o ka hepato- a me ka splenomanometry. Ho'opili'ia ka X-ray-hepatopathography, kahi e ho'ohemo'ia ai nā mea'oko'a i loko o nā ma'i hepatic. Ho'okumu'ia ka UZ-diagnostics ma nā kaha kiko'ī -'ike'ia ke koko i loko o nā'ōma'a.

Ma waho o kahi o nā hi'ohi'ona Doppler, hiki i kekahi ke lawe i ka ma'i Budda-Chiari me:

• ke alo aku o ka eiei? Loli ma ke akepaa, ano o ka loa momoma akepaʻa a me fibrosis o ke ake'aʻaʻa,

•'A'ole he ma'i heppa ma luna o ke ki'i, no ka la'ana, no ka hiki'ana i ka lumen o nā lehulehu echopositive i ka lumen,

• Ho'opili'ia ka pale i lalo,

• Nā hō'ailona o ka pi'i'ana o ka portal inā mau ka ma'i no ka manawa lō'ihi.