Ola kinoMaʻi a me nā kūlana

Wegener ka granulomatosis - 'ehaʻeha ka, symptoms, lapaau.

Wegener ka granulomatosis - mea he autoimmune maʻi wehewehe aku ma ka li nui o na arteries liilii, a me ka aa koko. Ma ka hapanui o na hihia i ka wela ai artery hoolako koko sinuses, akemāmā a me nā konāhua nā'aʻaʻa akā, ma ka hou, eia ka helehelena kinona i loko o ka hanana e loli ai wale i kekahi o kēia mau cii. Me ka nui granulomatosis kokoke mau mahaloʻia e nā na maʻiʻaʻai a me nā puʻupaʻaʻelua. Ma ia hihia, ina o ka iʻa e wale malamalama ole wale nā puʻupaʻa, ia mea he maʻi i kapaia o Wegener ka granulomatosis kāpili.

Wegener ka granulomatosis mea loa, he pono ole i loko o kanaka kaikaina a iwaena-elemakule, aneane me ke ku e na keiki. Akā, aka hoi, i ka maʻi mea hiki ke aloha ia a pau makahiki pūʻulu. Hoohanau 'ikepili helu hoʻolilo i kēia maʻi i kekahi i loko o kekahi kākau.

Nā kumu o ka maʻi

Nā kumu o ka maʻi, e like me Wegener ka granulomatosis, uaʻaʻole maopopo hoomaopopo i keia la. manaʻo nui nā akamai i ke kumu o ka maʻi i e ka mea hoʻomaʻi Agena, no ka mea, Wegener ka granulomatosis pinepine ia lŘlŘ ma hope o vaccination, SARS, antibiotic Inc paha waiū. Akā, Eia naʻe, i ka microbial Agena ua nō,ʻaʻole anao? Aou, no laila, i ka maʻi ua noʻonoʻo pono i autoimmune.

Kekahi nā mea maʻi i hookahuli ai poradenitis a me Wegener ka granulomatosis. E hoʻomaopopo ana aʻo Kīwala'ō o na symptoms, he mau maʻi loa okoa no ka poradenitis aicieeaao ma muli o ia mea koʻohune pathogens (Chlamydia), iā Wegener ka granulomatosis mea he autoimmune maʻi.

Symptoms a me ka maʻi ahulau ke ano

Wegener ka granulomatosis hiki hoʻomaka koke, akā, e flare i ke kiʻekiʻe. Ka mua symptom o ka maʻi hiki ke manao ia subfebrile wela, a laila, e emi kona'ōpū. Hope a ka mahana, e ala hou, a me ka maʻi holomua.

Na na symptoms o kēia maʻi nā:

- ke kaupaona poho;

- luhi;

- e hoohaunaele ana i ka wela;

-ʻeha i loko o na ami;

-ʻeha ma ka sinus li nui.

Eia hou, i ka maʻi hiki loli likeʻole māhele o ke kino, e hāʻawi ana i ka pono okoa symptoms. No ka laʻana, a me ke pio o ka mea mawaho naehana runny ihu me kaʻawaʻawa loa purulent koko mahele ana, necrotic nasal mucosa, e like me kaʻaeʻae kīleo a me tonsils.

A generalized ano o ka maʻi, oia he mau mahina, he complication nui o kaʻili, ma ka nui, ka ikeia o kahe ana ke koko, nodular, necrotic hehee wale, a ma kekahi pūʻulu o nā mea maʻi, a me ka pericarditis, myocarditis paha bronchitis.

ʻike, no ka maʻi

Kuhikuhi no kēia Wegener ka granulomatosis nā mea maʻi e hele urinalysis no ke alo o ke kumuʻiʻo a me kaʻulaʻula koko aeee i loko o ka mimi. E möakäka hou X-Ray kiʻi i i sinuses a me ka umauma, e ike i ka pathological hoʻololi. A, Ka Ikepili o ke koko ka i lawe ia, a, ma ka hana, me ka nānā 'ana ESR a me C-kū'ē kumuʻiʻo. Aia Ua hoi he oi eiiieaen, akā, i nui ka hoʻokō Ka Ikepili e hōʻike antineyrofilnyh cytoplasmic nā mea'aʻaʻa.

lapaau ana i ka maʻi

Wegener ka granulomatosis, me ka pono lapaau i ka hoʻomanawanui e pono e alakai i ka make i loko o elua a hiki i na malama ekolu. All iapaau ana uaʻano nui nona ma ka suppression o ka'ōnaehana paleʻea oihana, e like me kūloko hoʻoʻino reactions. Ka loa Popular ai 'i corticosteroids a me cyclophosphamide. Mau ai 'E e ia a hiki i ke kala ana o ka maʻi, a laila, i ole relapsed Hodgkin ka maʻi, hiki e hoʻokomo iā ia i a me ka methotrexate, a e lawe i ka mau o ka makahiki.

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